Ultrastructure and Peroxidase of Leucocytes in Five Patients with Juvenile form of Ceroid Lipofuscinoses

  • M. Daria Haust
  • Bruce A. Gordon
  • George G. Hinton
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 68)


In the past decade several advances have been made regarding the nature of diseases formerly known as amaurotic familial idiocies (API). This group was characterized clinically by cerebroretinal degenerations and morphologically by the accumulation of heterogeneous substances, all believed to have some lipid component.


Fingerprint Image Juvenile Form Batten Disease Juvenile Type Peripheral Leucocyte 
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Copyright information

© Plenum Press, New York 1976

Authors and Affiliations

  • M. Daria Haust
    • 1
    • 2
  • Bruce A. Gordon
    • 1
    • 2
  • George G. Hinton
    • 1
    • 2
  1. 1.The Departments of Pathology, Biochemistry and Pediatrics CPRILondonCanada
  2. 2.The University of Western OntarioLondonCanada

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