Hereditary Fructose Intolerance

  • Daniel Alagille
Part of the Hepatology book series (H, volume 5)


Hereditary fructose intolerance is the result of a congenital deficiency in fructose-1-phosphate aldolase and is transmitted by an autosomal recessive gene (1).


Acute Liver Failure Pyloric Stenosis Biliary Tract Disease Renal Tubular Dysfunction Congenital Deficiency 
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Copyright information

© Plenum Press, New York 1983

Authors and Affiliations

  • Daniel Alagille
    • 1
  1. 1.Unité de Recherche d’Hépatologie Infantile, INSERM U 56 & Clinique de PédiatrieUniversité Paris-Sud Hôpital d’EnfantsBicêtreFrance

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