Extrahepatic Biliary Atresia: Clinical Aspects

  • Daniel Alagille
Part of the Hepatology book series (H, volume 5)


The early diagnosis between intra- and extra-hepatic cholestasis is essential since the latter can be treated surgically. Until a few years ago, there were arguments against such an approach: these included the “non correctability” of extrahepatic biliary atresia, the rare occurrence of other forms of extrahepatic chole stasis and the adverse effects of surgery in patients with intra hepatic cholestasis. Surgery was performed only in cases of unresolved cholestasis after several months of evolution. This attitude has been challenged recently because surgical treatment of extrahepatic biliary atresia is available and positive results of surgical therapy are related to early intervention.


Biliary Atresia Choledochal Cyst Intrahepatic Cholestasis Portal Fibrosis Percutaneous Liver Biopsy 
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Copyright information

© Plenum Press, New York 1983

Authors and Affiliations

  • Daniel Alagille
    • 1
  1. 1.Unité de Recherche d’Hépatologie Infantile, INSERM U 56 & Clinique de PédiatrieUniversité Paris-Sud Hôpital d’EnfantsBicêtreFrance

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