Portacaval Shunt in Two Patients with Homozygous Hypercholesterolemia

  • E. A. Stein
  • C. Mieny
  • J. Pettifor
  • M. Dinner
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 63)


Despite the fact that the homozygous form of familial hyperbetalipoproteinemia (HβLP) is exceedingly rare, 17 such patients (from fourteen families) have been seen at a treatment centre for lipid disorders in Johannesburg during the past three years.


Nicotinic Acid Serum Cholesterol Achilles Tendon Lipid Disorder Portacaval Shunt 
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Copyright information

© Plenum Press, New York 1975

Authors and Affiliations

  • E. A. Stein
    • 1
    • 2
    • 3
  • C. Mieny
    • 4
    • 5
  • J. Pettifor
    • 2
    • 3
  • M. Dinner
    • 2
    • 3
  1. 1.Cardiovascular Research UnitSouth African Institute for Medical ResearchJohannesburgSouth Africa
  2. 2.Lipid Disorders Clinic, Departments of Pediatrics and Pediatric SurgeryUniversity of WitwatersrandJohannesburgSouth Africa
  3. 3.Transvaal Memorial Hospital for ChildrenJohannesburgSouth Africa
  4. 4.Department of SurgeryUniversity of WitwatersrandJohannesburgSouth Africa
  5. 5.J. G. Strydom HospitalJohannesburgSouth Africa

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