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Type III Hyperlipoproteinemia

  • Josef R. Patsch

Abstract

Several synonyms for familial type III hyperlipoproteinemia are often used. These include familial “broad-β” disease, “floating-β” disorder, dysbetalipoproteinemia, xanthoma tuberosum, and idiopathic hypercholesterolemic xanthomatosis with hyperlipemia. Type III hyperlipoproteinemia is a genetically determined lipoprotein disorder manifested by an increased concentration of both cholesterol and triglyceride in the plasma. It is characterized by the presence of a lipoprotein that floats between density 1.006–1.019 in the postabsorptive state. Moreover, the concentration of VLDL (d < 1.006) is increased, and, frequently, chylomicrons are present in the fasting plasma. Often, the plasma lipoprotein electrophoresis pattern is characterized by a “broad-β” band.

Keywords

High Density Lipoprotein Intermediate Density Lipoprotein Flotation Rate Lipoprotein Pattern Zonal Rotor 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Plenum Press, New York 1976

Authors and Affiliations

  • Josef R. Patsch
    • 1
  1. 1.Medical DepartmentUniversity of InnsbruckInnsbruckAustria

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