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Nutritional Management

  • Diane D. Stadler

Abstract

Two extremes of inappropriate growth impact on the nutritional management of individuals with Prader-Willi syndrome (PWS): failure to thrive and morbid obesity. Infants with PWS present to parents and medical personnel as hypotonic, with insufficient suck and swallow reflexes, and failure to thrive. Sometime after 1 year of age, children display the features of short stature, hyperphagia, and obesity, and demonstrate insatiable, nonselective appetites. Left untreated, adolescents or adults may develop respiratory distress, cyanosis, or sleep apnea secondary to massive obesity.

Keywords

Caloric Intake Dietary Recommendation Skinfold Thickness Recommend Dietary Allowance Nutritional Management 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© The Prader-Willi Syndrome Association 1988

Authors and Affiliations

  • Diane D. Stadler

There are no affiliations available

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