Two extremes of inappropriate growth impact on the nutritional management of individuals with Prader-Willi syndrome (PWS): failure to thrive and morbid obesity. Infants with PWS present to parents and medical personnel as hypotonic, with insufficient suck and swallow reflexes, and failure to thrive. Sometime after 1 year of age, children display the features of short stature, hyperphagia, and obesity, and demonstrate insatiable, nonselective appetites. Left untreated, adolescents or adults may develop respiratory distress, cyanosis, or sleep apnea secondary to massive obesity.
KeywordsCaloric Intake Dietary Recommendation Skinfold Thickness Recommend Dietary Allowance Nutritional Management
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