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Neurochemical Aspects of Mucopolysaccharidoses

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Handbook of Neurochemistry

Abstract

Mucopolysaccharidoses are defined in this chapter as inherited disorders, which result in the abnormal accumulation of mucopolysaccharides or glycoproteins in the body. This definition, somewhat broader than conventional, is adopted because the line between mucopolysaccharides and glycoprotein is becoming more and more obscure, and because there are disorders of glycoprotein metabolism which will not otherwise be covered in the Handbook. Several excellent reviews describe the chemistry and biochemistry of mucopolysaccharides and glycoproteins(1–8)

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  1. Department of Neurology, University of Pennsylvania School of Medicine, Philadelphia, Pennsylvania, USA

    Kunihiko Suzuki

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  1. Neurochemistry and Drug Addiction, New York State Research Institute, Ward’s Island, New York, New York, USA

    Abel Lajtha

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Suzuki, K. (1972). Neurochemical Aspects of Mucopolysaccharidoses. In: Lajtha, A. (eds) Handbook of Neurochemistry. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-7172-8_2

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