Postoperative Management after First-Stage Palliation

  • Gil Wernovsky
  • Doff B. McElhinney
  • Sarah Tabbutt
Part of the Developments in Cardiovascular Medicine book series (DICM, volume 246)


Survival and functional outcome of patients with HLHS have steadily continued to improve over the past 10-15 years. The majority of the mortality risk for patients undergoing staged reconstruction for HLHS occurs in the early postoperative period after Stage I palliation; early mortality in the current era has decreased to 10-15% or less at many centers [1, 2, 3]. Multiple factors have contributed to this progress, including developments in preoperative, operative, and postoperative management. The purpose of this chapter is to describe the approach to postoperative management currently employed at The Children’s Hospital of Philadelphia after first-stage reconstruction for HLHS, which is based on a philosophy of optimizing effective systemic oxygen delivery and minimizing systemic oxygen consumption, anticipating common pathophysiologic occurrences, and decreasing the potential for iatrogenic complications.


Pulmonary Vascular Resistance Pulmonary Blood Flow Hypoplastic Left Heart Syndrome Systemic Blood Flow Systemic Oxygen Delivery 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media New York 2003

Authors and Affiliations

  • Gil Wernovsky
    • 1
  • Doff B. McElhinney
    • 2
  • Sarah Tabbutt
    • 3
  1. 1.Divisions of CardiologyThe Children’s Hospital of PhiladelphiaBostonUSA
  2. 2.Department of CardiologyThe Children’s HospitalBostonUSA
  3. 3.Divisions of CardiologyThe Children’s Hospital of PhiladelphiaUSA

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