Anesthetic Management for HLHS

  • James M. Steven
  • Susan C. Nicolson
Part of the Developments in Cardiovascular Medicine book series (DICM, volume 246)


Optimal anesthetic management of infants and children with hypoplastic left heart syndrome (HLHS) entails a thorough understanding of the spectrum of anatomic and physiologic findings that can comprise this syndrome. Over the past two decades, a substantial amount has been learned about the unique considerations and challenges posed by patients with HLHS [1]. Some of these new concepts have been beneficial in the management of other forms of critical neonatal congenital heart disease (CHD), while others are nuances that uniquely apply to this malformation, the largest anatomic subset of patients with functional single ventricle.


Pulmonary Blood Flow Anesthetic Management Hypoplastic Left Heart Syndrome Systemic Arterial Pressure Noncardiac Surgery 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media New York 2003

Authors and Affiliations

  • James M. Steven
    • 1
  • Susan C. Nicolson
    • 1
  1. 1.Department of AnesthesiaChildren’s Hospital of PhiladelphiaUSA

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