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Univentricular Heart

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Cardiac CT and MR for Adult Congenital Heart Disease

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Abstract

A univentricular heart, or univentricular atrioventricular (AV) connection (UAVC), is not a single lesion but a broad term encompassing congenital malformations leading to a single ventricular physiology, a very rare condition where one dominant ventricle supports both circulations. Tricuspid atresia is the classic example and the most common variety of UAVC. Other varieties include double-inlet right or left ventricle, mitral atresia, hypoplastic left heart syndrome, unbalanced common AV canal, pulmonary atresia, and heterotaxy syndromes. Heterotaxy syndromes refer to disorders of lateralization whereby the arrangement of abdominal and thoracic viscera differ from normal and mirror image of normal (Khairy et al., Circulation 115:800–812, 2007).

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Authors and Affiliations

  1. Non-Invasive Cardiology Service and Adult Congenital Heart Disease Center, Montreal Heart Institute, 5000 Bélanger Street, Montreal, QC, H1T 1C8, Canada

    François-Pierre Mongeon MD, SM & François Marcotte MD, FRCPC

  2. Electrophysiology Service and Adult Congenital Heart Disease Center, Montreal Heart Institute, 5000 Bélanger Street, Montreal, QC, H1T 1C8, Canada

    Paul Khairy MD, PhD

Authors
  1. François-Pierre Mongeon MD, SM
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  2. François Marcotte MD, FRCPC
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  3. Paul Khairy MD, PhD
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Correspondence to Paul Khairy MD, PhD .

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Editors and Affiliations

  1. Department of Radiology, USC University Hospital Keck School of Medicine, Los Angeles, California, USA

    Farhood Saremi

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Mongeon, FP., Marcotte, F., Khairy, P. (2014). Univentricular Heart. In: Saremi, F. (eds) Cardiac CT and MR for Adult Congenital Heart Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8875-0_11

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  • DOI: https://doi.org/10.1007/978-1-4614-8875-0_11

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