Abstract
Hereditary angioedema has a bimodal distribution with peak incidences in the second and fourth decades and is characterized by local swelling in subcutaneous tissues. Diagnosis must generally be made during an acute episode1.
The most common gastrointestinal (GI) symptoms are:
Vomiting particularly early in attack
Acute severe abdominal pain; <24 h up to 5 days
Can also present with chronic recurring abdominal pain
Diarrhea, usually watery
Nausea
Prodromal phase including increased irritability, aggressiveness, fatigue, hunger
Clinical signs and findings include:
Bowel edema
Usually hypoactive bowel sounds, can be hyperactive
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Uddeen, J. (2013). Hereditary Angioedema: Gastrointestinal Features. In: Wu, G., Selsky, N., Grant-Kels, J. (eds) Atlas of Dermatological Manifestations of Gastrointestinal Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6191-3_53
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DOI: https://doi.org/10.1007/978-1-4614-6191-3_53
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