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Heart Valves pp 45–72Cite as

Congenital Heart Defects That Include Cardiac Valve Abnormalities

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Abstract

This chapter introduces the reader to the spectrum of congenital heart malformations that are associated with abnormalities of the cardiac valves. The author’s intent is to describe the basic structural anatomy of the cardiac valves, the pathologic features and clinical manifestations of common abnormalities that affect them, the indications and timing of surgical intervention, and the surgical techniques used for repair.

This chapter begins with a brief review of the embryology of the heart with emphasis on the development of the cardiac valves. The remainder of the chapter discusses congenital, rather than acquired, atrioventricular and semilunar valve abnormalities. The chapter ends with a brief description of congenital cardiac malformations where cardiac valve pathology is secondary to the underlying abnormality (i.e., Tetralogy of Fallot).

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Abbreviations

ASD:

Atrial septal defect

CAVC:

Complete atrioventricular canal

LV:

Left ventricular

PAIVS:

Pulmonary atresia with intact ventricular septum

PGE:

Prostaglandin E1

VSD:

Ventricular septal defect

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Authors and Affiliations

  1. Department of Surgery, University of Minnesota, 2450 Riverside Avenue, 8951F, Minneapolis, MN, 55454, USA

    Roosevelt Bryant III MD

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  1. Roosevelt Bryant III MD
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Correspondence to Roosevelt Bryant III MD .

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Editors and Affiliations

  1. , Mail Code 195, University of Minnesota, Delaware St. SE., 420, MINNEAPOLIS, 55455, Minnesota, USA

    Paul A. Iaizzo

  2. University of Minnesota, DELAWARE ST SE MMC 195 420, MINNEAPOLIS, 55455, Minnesota, USA

    Richard W. Bianco

  3. University of Minnesota, Department of Surgery, Medtronic, Inc., N/A, Minneapolis, 55432, Minnesota, USA

    Alexander J. Hill

  4. University of Minnesota, N/A, Minneapolis, 55455, Minnesota, USA

    James D. St. Louis

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Bryant, R. (2013). Congenital Heart Defects That Include Cardiac Valve Abnormalities. In: Iaizzo, P., Bianco, R., Hill, A., St. Louis, J. (eds) Heart Valves. Springer, Boston, MA. https://doi.org/10.1007/978-1-4614-6144-9_3

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