Sarcomas of bone are a rare and diverse set of tumors that, although related in their primary location (bone), vary in their etiology, behavior, and treatment. In 2011, approximately 2,890 new cases of bone and joint cancers were diagnosed in the USA. Osteosarcoma, chondrosarcoma, and Ewing sarcoma are the most common primary tumors of bone, representing 30 %, 15 %, and 6 %, respectively, of all bone sarcomas. The remainder of bone sarcomas is made up of malignant fibrous histiocytoma, chordoma, adamantinoma, hemangioendothelioma, hemangiopericytoma, and low-grade fibrosarcoma of the bone.


Limb Salvage Ewing Sarcoma Bone Sarcoma Werner Syndrome Limb Salvage Surgery 
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Copyright information

© Springer Science+Business Media New York 2013

Authors and Affiliations

  1. 1.Department of Orthopaedic OncologyThe University of Texas MD Anderson Cancer CenterHoustonUSA

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