Mostly Benign/Rarely Metastasizing Soft Tissue Tumor
Ossifying fibromyxoid tumor (OFMT) is a very uncommon soft tissue lesion that can occur anywhere in the body but most commonly in the lower extremity. While most tumors are benign, malignant examples may metastasize in more than half of cases . The largest series to date included only typical cases, excluding tumors with other morphologies, and in that series there were no patients who developed metastatic disease. In the few patients that we have observed recurrences, metastases are observed, typically to lung, and local-regional recurrence can be observed in a multifocal “shotgun” pattern around the area of the tumor, as has been observed in patients with epithelioid sarcoma.
KeywordsSynovial Sarcoma Pleomorphic Adenoma Giant Cell Tumor Glomus Tumor Epithelioid Sarcoma
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