Ocular Cicatricial Pemphigoid

  • Mark R. LevineEmail author


Cicatricial pemphigoid (mucous membrane pemphigoid) is a chronic autoimmune disease of unknown etiology that mainly affects mucous membranes showing conjunctival involvement in about 70% of cases. Skin lesions occur in 10–24% of patients [1]. It is a bilateral sight-threatening disease characterized by progressive conjunctival cicatrization associated with secondary corneal neovascularization and scarring. The disease usually presents between the ages of 30 and 90 years [2].


Bullous Pemphigoid Hemorrhagic Cystitis Benzalkonium Chloride Basement Membrane Zone Keratoconjunctivitis Sicca 
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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  1. 1.Department of OphthalmologyUniversity Hospitals of Cleveland, Cleveland Clinic FoundationClevelandUSA

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