Abstract
The Cornelia de Lange Syndrome (CDLS) is a mental retardation syndrome characterized by short stature, hirsutism, and facial and skeletal anomalies (de Lange, 1933, 1938; Hawley et al., 1985). It is interesting by virtue of association with a unique constellation of behavioral and temperamental attributes. One thinks first of self-injurious behavior (SIB), of course, and CDLS has been compared, in this regard, to the Lesch-Nyhan syndrome.
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© 1991 Springer-Verlag New York, Inc.
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Gualtieri, C.T. (1991). Behavior in the Cornelia de Lange Syndrome. In: Neuropsychiatry and Behavioral Pharmacology. Springer, New York, NY. https://doi.org/10.1007/978-1-4613-9036-7_8
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DOI: https://doi.org/10.1007/978-1-4613-9036-7_8
Publisher Name: Springer, New York, NY
Print ISBN: 978-0-387-97314-2
Online ISBN: 978-1-4613-9036-7
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