The Pathology of Univentricular Atrioventricular Connection

  • Robert H. Anderson
  • Siew Yen Ho
  • James R. Zuberbuhler
Conference paper


Lesions described according to the presumed singularity of their ventricular mass create problems in nomenclature and understanding. Included are hearts with double-inlet ventricle and those with atrioventricular valve atresia. In recent years, along with various colleagues [1–3], we have argued that all hearts with double-inlet should be considered (in terms of ventricular morphology) along with those having the type of atrioventricular valve atresia, which is characterized by absence of one atrioventricular connection. Critics said that our anatomic concept was flawed, because we used double-inlet atrioventricular connection as our unifying hallmark. In fact, the morphologic concept we promoted was entirely accurate. The confusion related to our illogical and meaningless use of the adjective “univentricular” (or “single”) to describe the ventricular mass in hearts that obviously possessed two ventricles. The resolution of this problem is simple and effective: to apply the adjective “univentricular” to the appropriate feature it describes—namely, the atrioventricular connection.


Tricuspid Atresia Univentricular Heart Ventricular Morphology Atrioventricular Junction Atrial Chamber 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media New York 1986

Authors and Affiliations

  • Robert H. Anderson
  • Siew Yen Ho
  • James R. Zuberbuhler

There are no affiliations available

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