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Management of orbital rhabdomyosarcoma

  • Moody D. WharamJr.
  • Harold M. Maurer
Part of the Cancer Treatment and Research book series (CTAR, volume 32)

Abstract

Rhabdomyosarcoma (RMS) is a soft tissue sarcoma that arises from the same mesodermal tissues that form striated skeletal muscle. It typically arises in the pediatric age group and can originate in virtually any anatomic location. The management of the child with orbital or eyelid RMS has changed substantially in the past two decades. Formerly dismal, the prognosis is now excellent. Advances have resulted from the application of two modern concepts in cancer management: first, multidisciplinary management including surgery, radiation oncology, and pediatric oncology; second, application of the methodology of the clinical research cooperative group. Principles of diagnostic evaluation, local tumor control, and treatment of disseminated but occult metastases have been developed and refined. Important information regarding etiology, histologic subtypes, treatment, and late effects continues to accrue.

Keywords

Local Recurrence Rate Local Tumor Control Tumor Dose Orbital Tumor Embryonal Rhabdomyosarcoma 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Martinus Nijhoff Publishers, Boston 1987

Authors and Affiliations

  • Moody D. WharamJr.
  • Harold M. Maurer

There are no affiliations available

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