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Genetically Determined Cardiomyopathies in Neuromuscular Diseases

  • Chapter
Heart Hypertrophy and Failure

Part of the book series: Developments in Cardiovascular Medicine ((DICM,volume 169))

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Abstract

Most genetically determined neuromuscular diseases have an assoicated cardiomyopathy. In single gene disorders the primary step in their pathogeneses is the mutant gene. It follows that the primary cause of such cardiomyopathies generally is this very same mutant gene. Thus, the identification of genes causing neuromuscular diseases provides us with a rapidly growing list of gene products that when altered can cause cardiomyopathies.

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  1. Klaus Wrogemann
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  1. MRC Group in Experimental Cardiology Division of Cardiovascular Sciences St. Boniface General Hospital Research Centre Faculty of Medicine, University of Manitoba, 351 Taché Avenue, Winnipeg, Manitoba, R2H 2A6, Canada

    Naranjan S. Dhalla (Distinguished Professor), Grant N. Pierce (Professor), Vincenzo Panagia (Professor) & Robert E. Beamish (Professor Emeritus) (Distinguished Professor),  (Professor),  (Professor) &  (Professor Emeritus)

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Wrogemann, K. (1995). Genetically Determined Cardiomyopathies in Neuromuscular Diseases. In: Dhalla, N.S., Pierce, G.N., Panagia, V., Beamish, R.E. (eds) Heart Hypertrophy and Failure. Developments in Cardiovascular Medicine, vol 169. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-1237-6_3

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