The clinical evaluation and assignment of gender of rearing in a neonate with genital ambiguity has been described as a medical emergency. Although expeditious investigation should be undertaken, it is also important to recognize that the worst injustice that can be committed during the initial evaluation is assignment of an inappropriate gender of rearing that subsequently must be altered. When the infant is first evaluated, the family should be reassured that the child’s genitalia are in an incompletely developed state and, after the appropriate evaluation is complete, reconstruction can be completed.
KeywordsCongenital Adrenal Hyperplasia Urethral Sphincter Gonadal Dysgenesis Urogenital Sinus Urethral Meatus
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