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Current Management of Hypoplastic Left Heart Syndrome

  • Serafin Y. DeLeon
  • Michel N. Ilbawi
  • Katherine Tubeszewski
  • Tarek S. Husayni
  • Anthony F. Cutilletta

Abstract

A diminutive, nonfunctional left ventricle with aortic atresia or severe aortic stenosis and hypoplasia of the ascending aorta constitutes the main structural abnormality in hypoplastic left heart syndrome. The syndrome often presents early with catastrophic hemodynamic decompensation. It is the most common cause of cardiac death in the first week of life1 and usually affects newborns who are otherwise normal.1,2 Hypoplastic left heart syndrome remains a major medical and surgical challenge.

Keywords

Pulmonary Artery Right Ventricle Main Pulmonary Artery Pulmonary Blood Flow Hypoplastic Left Heart Syndrome 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag New York Inc. 1990

Authors and Affiliations

  • Serafin Y. DeLeon
  • Michel N. Ilbawi
  • Katherine Tubeszewski
  • Tarek S. Husayni
  • Anthony F. Cutilletta

There are no affiliations available

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