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Dental Aspects of Epidermolysis Bullosa

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Epidermolysis Bullosa

Abstract

Because the skin and teeth are both ectodermal in origin, it is not surprising they are similarly affected in many pathologic processes. This is well illustrated in epidermolysis bullosa (EB), a heterogeneous group of genetic disorders in which blistering of the skin and mucosa occur as a result of minor trauma.1–4 In many patients, chewing and eating may cause formation of painful oral blisters that severely compromise nutritional intake. In addition, primary dental abnormalities such as enamel defects predispose patients to caries development. In severely affected patients crippling deformities of the hands make it almost impossible to maintain adequate oral hygeine. In this chapter, we review the unique spectrum of intraoral problems faced by EB patients and discuss management guidelines.

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Authors
  1. John J. Putnam
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  2. George. W. Sferra Jr.
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Editor information

Editors and Affiliations

  1. Laboratory for Investigative Dermatology, The Rockefeller University, 1230 York Avenue, New York, NY, 10021-6399, USA

    Andrew N. Lin M.D.  & D. Martin Carter M.D., Ph.D.  & 

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© 1992 Springer-Verlag New York, Inc.

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Putnam, J.J., Sferra, G.W. (1992). Dental Aspects of Epidermolysis Bullosa. In: Lin, A.N., Carter, D.M. (eds) Epidermolysis Bullosa. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2914-8_14

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  • DOI: https://doi.org/10.1007/978-1-4612-2914-8_14

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4612-7717-0

  • Online ISBN: 978-1-4612-2914-8

  • eBook Packages: Springer Book Archive

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