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Cerebrovascular Diseases in Children pp 168–187Cite as

Sturge-Weber Disease

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Part of the book series: Principles of Pediatric Neurosurgery ((PRINCPEDIATR))

Abstract

Neural cutaneous syndromes constitute a rather heterogeneous group from a clinical standpoint. They include several distinct forms that have in common developmental anomalies of neural and other ectodermal structures; in particular, the brain, the skin, and the retina. In many of these syndromes, also known as phakomatoses and ectodermal dysplasias, visceral abnormalities are associated as well.1

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Authors
  1. Concezio Di Rocco
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Editors and Affiliations

  1. Northwestern University Medical Schoool, Chigago, Illinois, USA

    Anthony J. Raimondi M.D. (Professor of Surgery (Neaurosurgery) (Professor of Surgery (Neaurosurgery)

  2. Hôpital des Enfantes de la Timone, Rue Sainte Pierre, 13005, Marseille, France

    Maurice Choux M.D.

  3. Instituto di Neuochirurgia, Università Cattolica del Sacre Cuore, Largo Gemelli 8, 00168, Rome, Italy

    Concezio Di Rocco M.D.

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Rocco, C.D. (1992). Sturge-Weber Disease. In: Raimondi, A.J., Choux, M., Di Rocco, C. (eds) Cerebrovascular Diseases in Children. Principles of Pediatric Neurosurgery. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2800-4_13

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  • DOI: https://doi.org/10.1007/978-1-4612-2800-4_13

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