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Advances in Child Neuropsychology pp 119–171Cite as

Dementia in Childhood: Issues in Neuropsychological Assessment with Application to the Natural History and Treatment of Degenerative Storage Diseases

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Part of the Advances in Child Neuropsychology book series (CHILDNEUROPSYCH,volume 2)

Abstract

This chapter is about childhood dementia, a topic that has not received much attention from pediatric neuropsychologists. Many neuropsychologists are unfamiliar with disorders that result in loss of mental function in children, and commonly, early death. They are rare disorders and many child neuropsychologists may spend an entire career without seeing such children. Increasing numbers of cases are being identified with childhood dementia from pediatric HIV and from neurotoxins. The need to document the course of these various childhood disorders and the outcomes of treatment from a neuropsychological perspective, and the unique opportunity these disorders afford to further our knowledge of developmental changes in brain-behavior relationships necessitate careful study of the characteristics of childhood dementia.

Keywords

  • Bone Marrow Transplantation
  • Duchenne Muscular Dystrophy
  • Neuronal Ceroid Lipofuscinosis
  • Metachromatic Leukodystrophy
  • Subacute Sclerosing Panencephalitis

These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Authors
  1. Elsa G. Shapiro
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  2. Kimberly A. Klein
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Editors and Affiliations

  1. Division of Child and Adolescent Psychiatry, Vanderbilt University School of Medicine, 37212, Nashville, TN, USA

    Michael G. Tramontana Ph.D.

  2. Department of Psychiatry and the Clinical Center for the Study of Development and Learning, University of North Carolina School of Medicine, 27514, Chapel Hill, NC, USA

    Stephen R. Hooper Ph.D.

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Shapiro, E.G., Klein, K.A. (1994). Dementia in Childhood: Issues in Neuropsychological Assessment with Application to the Natural History and Treatment of Degenerative Storage Diseases. In: Tramontana, M.G., Hooper, S.R. (eds) Advances in Child Neuropsychology. Advances in Child Neuropsychology, vol 2. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2608-6_4

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