Myotonic Disorders

  • Carl D. Reimers
  • Thomas J. Vogl


Myotonic dystrophy was recognized to represent a specific disease by the German internist Hans Steinert1 and the British neurologists Fred Eustace Batten and H.P. Gibb2 in 1909. However, the characteristic combination of myotonia and distal muscle weakness was first described by the American physician C.L. Dana in 1888.3


Myotonic Dystrophy Rectus Femoris Fatty Change Open Arrow Medial Head 
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© Springer-Verlag New York, Inc. 1996

Authors and Affiliations

  • Carl D. Reimers
  • Thomas J. Vogl

There are no affiliations available

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