Glomus tumor is a rare benign neoplasm composed of cells derived from the smooth muscle cells that surround blood vessels in the glomus body. It can be multiple – glomangiomatosis. Most cases occur in the fingers, usually in a subungueal location. Feet are also a frequent site. Excruciating pain is the hallmark of this tumor. Radiographs show a lucent, well-defined nodular depression in the extremity of the distal phalanx. Tumor cells are round in glomus tumor but may be elongated, in glomangiomyoma. They are positive for smooth muscle markers. Marginal resection or curettage is curative for benign tumors. Malignant glomus tumors require multimodality cancer treatment.
KeywordsGlomus Glomangioma Vascular Perivascular Tumor Digits
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