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Constriction Ring Syndrome

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Disorders of the Hand

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Abstract

Constriction ring syndrome is a rare condition of unknown etiology. Numerous names have been used to describe this entity in the past including annular band syndrome, constriction band syndrome, Streeter dysplasia, Torpin dysplasia, amniotic band disruption sequence, acrosyndactyly, fenestrated syndactyly and congenital amputation syndrome [1]. The syndrome is characterized by bands of ranging severity, always present at birth, that can affect any part of the body with a particular predilection for the upper or lower extremities [2].

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Authors and Affiliations

  1. Department of Paediatric Hand Surgery, Great Ormond Street Hospital for Children, Great Ormond Street, London, WC1N 3JH, UK

    Bran Sivakumar MD (Res), FRCS (Plast)

  2. Royal Free Hospital, Pond Street, London, NW3 2QG, UK

    Bran Sivakumar MD (Res), FRCS (Plast)

  3. Department of Plastic and Hand Surgery, Great Ormond Street Hospital for Children, Great Ormond Street, London, WC1N 3JH, UK

    Paul Smith MBBS, FRCS

  4. The Portland Hospital for Women and Children, 205 – 209 Great Portland Street, London, W1W 5AH, UK

    Paul Smith MBBS, FRCS

Authors
  1. Bran Sivakumar MD (Res), FRCS (Plast)
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  2. Paul Smith MBBS, FRCS
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Correspondence to Paul Smith MBBS, FRCS .

Editor information

Editors and Affiliations

  1. Hall Lane, Appley Bridge, Wrightington Hospital, Wigan, Lancashire, United Kingdom

    Ian A. Trail

  2. St George's Hospital, London, United Kingdom

    Andrew N.M. Fleming

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Sivakumar, B., Smith, P. (2015). Constriction Ring Syndrome. In: Trail, I., Fleming, A. (eds) Disorders of the Hand. Springer, London. https://doi.org/10.1007/978-1-4471-6563-7_11

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  • DOI: https://doi.org/10.1007/978-1-4471-6563-7_11

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