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Congenital Aortic Valve Stenosis

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Comprehensive Approach to Adult Congenital Heart Disease

Abstract

Congenital aortic valve stenosis (AS) is a relatively common anomaly. Congenital AS occurs much more commonly in men, with a male to female ratio of 4:1. Related cardiac anomalies have been seen in up to 1/5 of patients. Patent ductus arteriosus (PDA) and coarctation of the aorta happen most often with AS [1].

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Correspondence to Azin Alizadehasl MD, FACC .

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310404_1_En_35_MOESM1_ESM.avi

Oval shape opening of the Bicuspid Aortic valve (BAV) in parasternal short-axis view, note the evaluation was done in systole (AVI 3618 kb)

Transesophageal echocardiography showing thickened and calcified BAV in short axis view (WMV 628 kb)

The catheter course is arterial; injection was performed in aortic root and showed doming of AV cusps due to bicuspid aortic valve (WMV 422 kb)

Quadricuspid aortic valve in short axis and long axis transesophageal echocardiography associated with significant aortic regurgitation (WMV 544 kb)

Quadricuspid aortic valve in short axis and long axis transesophageal echocardiography associated with significant aortic regurgitation (WMV 333 kb)

Video 35.1

Oval shape opening of the Bicuspid Aortic valve (BAV) in parasternal short-axis view, note the evaluation was done in systole (AVI 3618 kb)

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Alizadehasl, A., Sadeghpour, A. (2014). Congenital Aortic Valve Stenosis. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_35

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  • DOI: https://doi.org/10.1007/978-1-4471-6383-1_35

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-6382-4

  • Online ISBN: 978-1-4471-6383-1

  • eBook Packages: MedicineMedicine (R0)

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