The Malformed Eye

  • W. R. Lee


Basically, malformations of the eye, orbit and adnexa are encountered in three forms. First, there are ocular abnormalities of a relatively minor nature, e.g. colobomas and minor malformations of the nerve head and retina, which are observed in otherwise normal individuals and which do not require treatment. Secondly, there are those, e.g. corneal malformations, cataracts and vitreous disorders, which are amenable to surgical intervention and in which excised tissue may be submitted to the laboratory for investigation. Thirdly, there are those in which major or minor degrees of ocular malformation are associated with severe and often lethal systemic disorders, e.g. anencephaly and gross chromosomal abnormalities such as the trisomy D group; such abnormalities are encountered in the post-mortem room.


Retinal Pigment Epithelium Trabecular Meshwork Neural Retina Lamina Cribrosa Ciliary Muscle 
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Copyright information

© Springer-Verlag London 1993

Authors and Affiliations

  • W. R. Lee
    • 1
  1. 1.Department of PathologyUniversity of GlasgowGlasgowUK

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