This group of disorders consists of a number of different conditions in all of which the clinical phenomenon of myotonia occurs (Table 15.1). Becker (1971, 1977) ascertained the prevalence of the various myotonic syndromes in West Germany and noted the overwhelming predominance of myotonic dystrophy in 80% of the patients surveyed, although it is likely that his results were biased by reliance on hospital-based cases.
KeywordsSpinal Muscular Atrophy Myotonic Dystrophy Muscle Fibre Membrane Motor Conduction Velocity Intrafusal Muscle Fibre
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