Collagen Vascular Diseases

  • Joseph P. LynchIII
  • Jonathan B. Orens
  • Ella Kazerooni


Pleuropulmonary complications of collagen vascular disorders (CVDs) are protean, and include: pleuritis, pleural effusions, bronchiolitis obliterans (with or without organizing pneumonia), small airways disease, chronic interstitial pneumonitis/fibrosis, pulmonary hemorrhage, vasculitis, pulmonary hypertension, nodules, diaphragmatic weakness, and opportunistic infections or pulmonary toxicity due to immunosuppressive drug therapy [1–7] (Table 16.1). Given the emphasis of this book on diffuse lung disorders, we primarily focus on chronic interstitial lung disease (CILD), which may complicate any of the CVDs. We briefly allude to additional complications which are of special importance for some of the CVDs.


Pulmonary Hypertension Idiopathic Pulmonary Fibrosis Interstitial Lung Disease Systemic Sclerosis Lung Biopsy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag London Limited 1999

Authors and Affiliations

  • Joseph P. LynchIII
  • Jonathan B. Orens
  • Ella Kazerooni

There are no affiliations available

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