Renal Vascular Fibromuscular Dysplasia

Chapter

Abstract

Fibromuscular dysplasia of the renal arteries is an idiopathic, non-inflammatory form of renal artery stenosis causing renovascular hypertension in children and younger adults. It is defined by pathognomonic angiographic and histologic findings. The pathogenesis of this disorder is unknown and evidence supports the likelihood of heterogeneous etiologies for this disorder. It is an important potentially curable form of renovascular hypertension. This chapter will discuss the epidemiology, clinical associations, and presentations of fibromuscular dysplasia and review treatment approaches and outcomes.

Keywords

Fibromuscular dysplasia Renovascular hypertension Nonatherosclerotic renal artery disease Renal artery stenosis Renal artery aneurysm Non-inflammatory arteriopathy Segmental arterial mediolysis 

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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  1. 1.Renal Division, Department of MedicineBaystate Medical Center/Tufts New England Medical Center, Western New England Renal and Transplant AssociatesSpringfieldUSA

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