Pulmonary Valve Stenosis, Pulmonary Arterial Stenosis, and Isolated Right Ventricular Hypoplasia

  • L. N. Benson
  • R. M. Freedom


Obstruction of blood flow from right ventricle to pulmonary artery most frequently occurs at valve level. Infrequently, infundibular obstruction, hypoplasia of the trabecular portion of the right ventricle or pulmonary arterial stenosis are found in isolation, but uncommonly in isolation in the neonate. More commonly, the latter are components of more complex cardiac lesions such as Fallot’s tetralogy (Chapter 15), the so-called double-chambered right ventricle (Chapter 34), or pulmonary atresia and intact ventricular septum (Chapter 19). In this chapter, attention is paid to these lesions as they occur in “isolation”. We emphasize, as noted by Rowe et al. [77] and Anderson et al. [3], that these lesions are neither simple nor isolated, but have profound influences on other parts of the heart.


Pulmonary Artery Tricuspid Valve Pulmonary Valve Main Pulmonary Artery Pulmonary Stenosis 
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  • L. N. Benson
  • R. M. Freedom

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