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Neonatal Heart Disease pp 497–521Cite as

Hearts with a Univentricular Atrioventricular Connection

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Abstract

The ingenious contribution of Fontan and Baudet [35] has forever altered the natural history of the patient with functionally one ventricle. The application of an atriopulmonary connection and atrial partitioning to a patient in 1968 with tricuspid atresia opened the doors to potential longterm palliation for patients with a wide range of complex cardiac malformations [25, 60, 69]. This operation has effectively removed for many children the “Cinderella” stigma [17]. We will explore the clinical manifestations of the neonate with single ventricle, those methodologies that are diagnostic of this condition, and those surgical procedures that palliate and preserve the potential for Fontan’s operation. See also Chapter 19.

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References

  1. Albus RA, Trusler GA, Izukawa T, Williams WG (1984) Pulmonary artery banding. J Thorac Cardiovasc Surg 5: 645–653

    Google Scholar 

  2. Anderson RH, Arnold R, Thapar MK, Jones RS, Hamilton DI (1974) Cardiac specialized tissue in hearts with an apparently single ventricular chamber (double inlet left ventricle). Am J Cardiol 33: 95–106

    Article  PubMed  CAS  Google Scholar 

  3. Anderson RH, Becker AE, Wilkinson JL, Gerlis LM (1976) Morphogenesis of univentricular hearts. Br Heart J 37: 558–572

    Article  Google Scholar 

  4. Anderson RH, Becker AE, Freedom RM et al. (1979) Problems in the nomenclature of the univentricular heart. Herz 4: 97–106

    PubMed  CAS  Google Scholar 

  5. Anderson RH, Becker AE, Macartney FJ, Shinebourne EA, Wilkinson JL, Tynan MJ (1979) Is tricuspid atresia a univentricular heart? Pediatr Cardiol 1: 51–56

    Article  Google Scholar 

  6. Anderson RH, Tynan M, Freedom RM et al. (1979) Ventricular morphology in the univentricular heart. Herz 4: 176–183

    Google Scholar 

  7. Anderson RH, Becker AE, Tynan M, Macartney FJ, Rigby ML, Wilkinson JL (1982) The univentricular atrioventricular connection: getting to the root of a thorny problem. Am J Cardiol 54: 822–828

    Article  Google Scholar 

  8. Anderson RH, Lenox CC, Zuberbuhler JR, Ho SY, Smith A, Wilkinson JL (1983) Double-inlet left ventricle with rudimentary right ventricle and ventriculoarterial concordance. Am J Cardiol 52: 573–577

    Article  PubMed  CAS  Google Scholar 

  9. Anderson RH, Macartney FJ, Tynan M et al. (1983) Univentricular atrioventricular connection: the single ventricle trap unsprung. Pediatr Cardiol 4: 273–280

    Article  PubMed  CAS  Google Scholar 

  10. Anderson RH, Penkoske PA, Zuberbuhler JR (1985) Variable morphology of ventricular septal defect in double inlet left ventricle. Am J Cardiol 55: 1560–1565

    Article  PubMed  CAS  Google Scholar 

  11. Anderson RH, Crupi GC, Parenzan L (1987) Double inlet ventricle. Elsevier, New York, pp 3–71

    Google Scholar 

  12. Anderson RH, Macartney FJ, Shinebourne EA, Tynan M (1987) Paediatric cardiology vol 2. Churchill Livingstone, Edinburgh, pp 643–674

    Google Scholar 

  13. Barber G, Hagler DJ, Edwards WD et al. (1984) Surgical repair of univentricular heart (double inlet left ventricle) with obstructed anterior subaortic outlet chamber. J Am Coll Cardiol 4: 771–777

    Article  PubMed  CAS  Google Scholar 

  14. Bharati S, Lev M (1975) The course of the conduction system in single ventricle with inverted (L-) loop and inverted ( L-) transposition. Circulation 51: 723–730

    Google Scholar 

  15. Bharati S, Lev M (1979) The concept of tricuspid atresia complex as distinct from that of the single ventricle complex. Pediatr Cardiol 1: 57–62

    Article  Google Scholar 

  16. Bisset GS III, Hirschfeld SS (1983) The univentricular heart: combined 2-dimensional-pulsed Doppler ( Duplex) echocardiographic evaluation. Am J Cardiol 51: 1149–1154

    Google Scholar 

  17. Brock R (1964) Tricuspid atresia: a step toward corrective treatment. J Thorac Cardiovasc Surg 47: 17–25

    PubMed  CAS  Google Scholar 

  18. Cabrera A, Azcuna JI, Bilbao F (1974) Single primitive ventricle with D-transposition of the great vessels and atresia of the left A-V valve. Report of a case. Am Heart J 88: 225–228

    Google Scholar 

  19. Caspi J, Coles JG, Rabinovich M et al. (1990) Morpho-logical findings contributing to a failed Fontan procedure: twelve-year experience. Circulation 82 (Suppl IV): 177–182

    Google Scholar 

  20. Casta A, Wolf WJ, Sapire DW (1985) Absent right atrioventricular connexion with the left atrium connected to the morphologically right ventricle, a right-sided rudimentary left ventricle, and right juxtaposition of the atrial appendages: documentation by angiography and cross-sectional echocardiography. Int J Cardiol 7: 21–26

    Article  PubMed  CAS  Google Scholar 

  21. Chen S, Pennington DG, Nouri S, Sivakoff M, Fagan LF (1984) Management of infants with univentricular heart. Am Heart J 107: 1252–1256

    Article  PubMed  CAS  Google Scholar 

  22. Chin AJ, Barber G, Helton JG et al. (1988) Fate of pulmonic valve after proximal pulmonary artery-to-ascending aorta anastomosis for aortic outflow obstruction. Am J Cardiol 62: 435–438

    Article  PubMed  CAS  Google Scholar 

  23. Cifarelli A, Di Carlo D, Pasquini L, Narino B, Ballerini L (1989) Univentricular atrioventricular connection to a dominant left ventricle with a concordant ventriculoarterial connection. Int J Cardiol 25: 21–26

    Article  PubMed  CAS  Google Scholar 

  24. Corno A, Becker AE, Bulterijs AHK et al. (1975) Univentricular heart: can we alter the natural history? Ann Thorac Surg 19: 716–726

    Article  Google Scholar 

  25. de la Cruz MV, Miller BL (1968) Double-inlet left ventricle. Two pathological specimens with comments on the embryology and on its relation to single ventricle. Circulation 37: 249–260

    Google Scholar 

  26. De Leon SY, Ilbawi MN, Idriss FS et al. (1986) Fontan type operation for complex lesions. Surgical considerations to improve survival. J Thorac Cardiovasc Surg 92: 1029–1037

    Google Scholar 

  27. de Vivie R, Van Praagh S, Bein G, Eigster G, Vogt J, Van Praagh R (1989) Transposition of the great arteries with straddling tricuspid valve: Report of two rare cases with acquired subaortic stenosis after main pulmonary artery banding. J Thorac Cardiovasc Surg 98: 205–213

    PubMed  Google Scholar 

  28. Di Donato R, Dicarlo D, Giannico S, Marcelletti C (1989) Palliation of complex cardiac anomalies with subaortic stenosis: new operative approach. J Am Coll Cardiol 13: 406–412

    Article  PubMed  Google Scholar 

  29. Dick M, Fyler DC, Nadas AS (1975) Tricuspid atresia: clinical course in 101 patients. Am J Cardiol 36: 327–337

    Article  PubMed  CAS  Google Scholar 

  30. Dickinson DF, Smith A, Becker AE, Anderson RH (1979) Atrioventricular conduction tissues in univentricular hearts of left ventricular type with absent right atrioventricular connection (‘tricuspid atresia’). Br Heart J 42: 1–8

    Article  PubMed  CAS  Google Scholar 

  31. Doherty A, Ho SY, Anderson RH, Rigby ML (1989) Morphological nature of the atrioventricular valves in hearts with double inlet left ventricle. Pediatr Pathol 9: 521–529

    Article  PubMed  CAS  Google Scholar 

  32. Doty DB, Schieken RM, Lauer RM (1979) Septation of the univentricular heart. Transatrial approach. J Thorac Cardiovasc Surg 78: 423–430

    Google Scholar 

  33. Doty DB, Marvin WJ, Lauer RM (1981) Single ventricle with aortic outflow obstruction. Operative repair by creation of double outlet to the aorta and application of the Fontan principle. J Thorac Cardiovasc Surg 81: 636–640

    CAS  Google Scholar 

  34. Ebert PA, Turley K (1983) Surgery for cyanotic heart disease in the first year of life. J Am Coll Cardiol 1: 274–279

    Article  PubMed  CAS  Google Scholar 

  35. Elliott LP, Anderson RC, Edwards JE (1964) The common cardiac ventricle with transposition of the great vessels. Br Heart J 26: 289–301

    Article  PubMed  CAS  Google Scholar 

  36. Feldt RH, Mair DD, Danielson GK, Wallace RB, McGoon DC (1981) Current status of the septation procedure for univentricular heart. J Thorac Cardiovasc Surg 82: 93–97

    PubMed  CAS  Google Scholar 

  37. Fontan F, Baudet E (1971) Surgical repair of tricuspid atresia. Thorax 26: 240–248

    Article  PubMed  CAS  Google Scholar 

  38. Franklin RCG, Sullivan ID, Anderson RH, Shinebourne EA, Deanfield JE (1990) Is banding of the pulmonary trunk obsolete for infants with tricuspid atresia and double inlet ventricle with a discordant ventriculoarterial connection? Role of aortic arch obstruction and subaortic stenosis. J Am Coll Cardiol 16: 1455–1464

    Article  PubMed  CAS  Google Scholar 

  39. Freed MD, Rosenthal A, Plauth WH Jr, Nadas AS (1973) Development of subaortic stenosis after pulmonary artery banding. Circulation 47 and 48 (Suppl III): 7–10

    Google Scholar 

  40. Freedom RM (1981) The morphologic and therapeutic implications of an obstructive anomaly of the aortic arch in infants with complex congenital heart disease. In: Parenzan L, Crupi GC, Graham G (eds) Congenital heart disease in the first three months of life: medical and surgical aspects. Patron Editore, Bologna, pp 341–361

    Google Scholar 

  41. Freedom RM (1987) The dinosaur and banding of the main pulmonary trunk in the heart with functionally one ventricle and transposition of the great arteries: a saga of evolution and caution. J Am Coll Cardiol 10: 427–429

    Article  PubMed  CAS  Google Scholar 

  42. Freedom RM, Rowe RD (1978) Morphological and topographical variations of the outlet chamber in complex congenital heart disease: an angiographic study. Cathet Cardiovasc Diagn 4: 345–371

    Article  PubMed  CAS  Google Scholar 

  43. Freedom RM, Culham JAG, Rowe RD (1977) Angiocar-diograpy of subaortic obstruction in infancy. AJR 129: 813–824

    PubMed  CAS  Google Scholar 

  44. Freedom RM, Dische MR, Rowe RD (1977) Pathologic anatomy of subaortic stenosis and atresia in the first year of life. Am J Cardiol 39: 1035–1044

    Article  PubMed  CAS  Google Scholar 

  45. Freedom RM, Nanton M, Dische MR (1977) Isolated ventricular inversion with double-inlet left ventricle. Eur J Cardiol 5: 63–86

    PubMed  CAS  Google Scholar 

  46. Freedom RM, Sondheimer H, Dische R, Rowe RD (1977) Development of subaortic stenosis after pulmonary arterial banding for common ventricle. Am J Cardiol 39: 78–83

    Article  PubMed  CAS  Google Scholar 

  47. Freedom RM, Williams WG, Fowler RS, Trusler GA, Rowe RD (1980) Tricuspid atresia, transposition of the great arteries, and banded pulmonary artery. Repair by arterial switch, coronary artery reimplantation, and right atrioventricular valved conduit. J Thorac Cardiovasc Surg 80: 621–628

    Google Scholar 

  48. Freedom RM, Picchio F, Duncan WJ, Harder JR, Moes CAF, Rowe RD (1982) The atrioventricular junction in the univentricular heart: a two-dimensional echocardiographic analysis. Pediatr Cardiol 3: 105–117

    Article  PubMed  CAS  Google Scholar 

  49. Freedom RM, Culham JAG, Moes CAF (1984) Angiocardiography of congenital heart disease. Macmillan, New York, pp 593–628

    Google Scholar 

  50. Freedom RM, Benson LN, Smallhorn JF, Williams WG, Trusler GA, Rowe RD (1986) Subaortic stenosis, the univentricular heart, and banding of the pulmonary artery: an analysis of the courses of 43 patients with univentricular heart palliated by pulmonary artery banding. Circulation 73: 758–764

    Article  PubMed  CAS  Google Scholar 

  51. Friedman S, Edmunds H, Saraclar M, Weinstein EM (1976) Mitral atresia with premature closure of foramen ovale. A rare hemodynamic cause for failure of Blalock-Taussig anastomosis to relieve inadequate pulmonary blood flow. J Thorac Cardiovasc Surg 71: 118–122

    Google Scholar 

  52. Fyfe DA, Taylor AB, Gillette PC, Kline CH, Crawford FAJ (1987) Doppler echocardiographic confirmation of recurrent atrial septal defect stenosis in infants with mitral valve atresia. Am J Cardiol 60: 410–411

    Article  PubMed  CAS  Google Scholar 

  53. Fyler DC (1980) Report of the New England regional infant cardiac program. Pediatrics 65 (Suppl): 376–461

    Google Scholar 

  54. Garcia O, Wilkins R, Cunha D, Jesse MJ (1975) Left subclavian steal, interrupted aortic arch, complete transposition of the great vessels and single left ventricle. Chest 67: 352–354

    Article  PubMed  CAS  Google Scholar 

  55. Girod DA, Lima RC, Anderson RH, Ho SY, Rigby ML, Quaegebeur JM (1984) Double-inlet ventricle: morphologic analysis and surgical implications in 32 cases. J Thorac Cardiovasc Surg 88: 590–600

    PubMed  CAS  Google Scholar 

  56. Hallermann FJ, Davis GD, Ritter DG, Kincaid OW (1966) Roentgenographic features of common ventricle. Radiology 87: 409–423

    PubMed  CAS  Google Scholar 

  57. Horsley BL, Zuberbuhler JR, Bahnson H (1970) Factors influencing survival after banding of the pulmonary artery. A review of 89 cases. Arch Surg. 101: 776–779

    Article  PubMed  CAS  Google Scholar 

  58. Huhta JC, Maloney JD, Ritter DG, Ilstrup DM, Feldt RH (1983) Complete atrioventricular block in patients with atrioventricular discordance. Circulation 67: 1374–1377

    Article  PubMed  CAS  Google Scholar 

  59. Jimenez MQ, Sonnenfeld IR (1974) Anomalias obstruc-tivas del arco aortico en el ventriculo unico izquierdo. Rev Esp Cardiol 27: 113–120

    Google Scholar 

  60. Jimenez MQ, Martinez VP, Guzman MS, Alonso MR, Diaz LP (1975) Alterations des valvules auriculo-ventriculaires dans les ventricules uniques et anomalies similaires. Arch Mai Coeur 8: 823–832

    Google Scholar 

  61. Jonas RA, Castaneda AR, Lang P (1985) Single ventricle (single-or double-inlet) complicated by subaortic stenosis: surgical options in infancy. Ann Thorac Surg 39: 361–365

    Article  PubMed  CAS  Google Scholar 

  62. Keeton BR, Macartney FJ, Hunter S et al. (1979) Univentricular heart of right ventricular type with double or common inlet. Circulation 59: 403–411

    PubMed  CAS  Google Scholar 

  63. Kirklin JK, Blackstone EH, Kirklin JW, Pacifico AD, Bargeron LM (1986) The Fontan operation. Ventricular hypertrophy, age, and date of operation as risk factors. J Thorac Cardiovasc Surg 92: 1049–64

    Google Scholar 

  64. Kozuka T, Sako K, Fujino M, Kawashima Y, Nosaki T (1973) Roentgenographic diagnosis of single ventricle. Analysis of 42 cases. AJR 119: 512–523

    CAS  Google Scholar 

  65. Kuroda O, Sano T, Matsuda H et al. (1987) Analysis of the effects of the Blalock-Taussig shunt on ventricular function and the prognosis in patients with single ventricle. Circulation 76 (Suppl III): 24–28

    Google Scholar 

  66. Lev M, Liberthson RR, Kirkpatrick JR, Eckner FAO, Arcilla RA (1969) Single (primitive) ventricle. Circulation 39: 577–591

    PubMed  CAS  Google Scholar 

  67. Liberthson RR, Hastreiter AR, Sinha SN, Bharati S, Novak G, Lev M (1973) Levocardia with visceral heterotaxy -isolated levocardia: pathologic anatomy and its clinical implications. Am Heart J 85: 40–54

    Article  PubMed  CAS  Google Scholar 

  68. Lin AE, Laks H, Barber G, Chin AJ, Williams RG (1986) Subaortic obstruction in complex congenital heart disease: management by proximal pulmonary artery to ascending aorta end to side anastomosis J Am Coll Cardiol 7: 617–624

    CAS  Google Scholar 

  69. Macartney FJ, Partridge JB, Scott O, Deverall PB (1976) Common or single ventricle. An angiographic and hemodynamic study of 42 patients. Circulation 53: 543–552

    PubMed  CAS  Google Scholar 

  70. Marin-Garcia J, Tandon R, Edwards JE (1974) Single ventricle with transposition. Circulation 49: 994–1004

    PubMed  CAS  Google Scholar 

  71. Marin-Garcia J, Tandon R, Moller JH, Edwards JE (1974) Common (single) ventricle with normally related great vessels. Circulation 49: 565–573

    PubMed  CAS  Google Scholar 

  72. Mayer JE, Helgason H, Jonas RA et al. (1986) Extending the limits for modified Fontan procedures. J Thorac Cardiovasc Surg 92: 1021–1028

    PubMed  Google Scholar 

  73. McKay R, Pacifico AD, Blackstone EH, Kirklin JW, Bargeron LMJ (1982) Septation of the univentricular heart with left anterior subaortic outlet chamber. J Thorac Cardiovasc Surg 84: 77–87

    PubMed  CAS  Google Scholar 

  74. Mickell JJ, Mathews RA, Park SC et al. (1980) Left atrioventricular valve atresia: clinical management. Circulation 61: 123–127

    PubMed  CAS  Google Scholar 

  75. Mietus-Snyder M, Lang P, Mayer JE, Jones RA, Castaneda AR, Lock JE (1987) Childhood systemic-pulmonary shunts: subsequent suitability for Fontan operation. Circulation 76 (Suppl III): 39–44

    Google Scholar 

  76. Moak JP, Gersony WM (1987) Progressive atrioventricular valvular regurgitation in single ventricle. Am] Cardiol 59: 656–658

    Article  CAS  Google Scholar 

  77. Moodie DS, Ritter DG, Tajik AH, O’Fallon WM (1984) Long-term follow-up of unoperated patients with univentricular heart. Am J Cardiol 53: 1124–1128

    Article  PubMed  CAS  Google Scholar 

  78. Moodie DS, Ritter DG, Tajik AH, McGoon DC, Danielson GK, O’Fallon, WM (1984) Long-term follow-up after palliative operation for univentricular heart. Am J Cardiol 53: 1648–1651

    Article  PubMed  CAS  Google Scholar 

  79. Moreno-Cabral RJ, Miller DC, Oyer PE, Stinson EB, Reitz BA, Shumway NE (1980) A surgical approach for S,L,L single ventricle incorporating total right atrium-pulmonary artery diversion. J Thorac Cardiovasc Surg 79: 202–210

    PubMed  CAS  Google Scholar 

  80. Neches WH, Park SC, Lenox CC, Zuberbuhler JR, Bahnson HT (1973) Tricuspid atresia with transposition of the great arteries and closing ventricular septal defect. Successful palliation by banding of the pulmonary artery and creation of an aorticopulmonary window. J Thorac Cardiovasc Surg 4: 538–542

    Google Scholar 

  81. Norwood WI, Lang P, Castaneda AR, Murphy JD (1983) Management of infants with left ventricular outflow obstruction by conduit interposition between the ventricular apex and thoracic aorta. J Thorac Cardiovasc Surg 86: 771–776

    PubMed  CAS  Google Scholar 

  82. Oldham HNJ, Kakos GS, Jarmakani JM, Sabiston DC (1972) Pulmonary artery banding in infants with complex congenital heart defects. Ann Thorac Surg 13: 342–350

    Article  PubMed  Google Scholar 

  83. Park SC, Siewers RD, Neches WH et al. (1984) Surgical management of univentricular heart with subaortic stenosis. Ann Thorac Surg 37: 417–421

    Article  PubMed  CAS  Google Scholar 

  84. Penkoske PA, Freedom RM, Williams WG, Trusler GA, Rowe RD (1984) Surgical palliation of subaortic stenosis in the univentricular heart. J Thorac Cardiovasc Surg 87: 767–781

    PubMed  CAS  Google Scholar 

  85. Perry SB, Lang P, Keane JF, Jonas RA, Sanders SP, Lock JE (1986) Creation and maintenance of an adequate interatrial communication in left atrioventricular valve atresia or stenosis. Am J Cardiol 58: 622–626

    Article  PubMed  CAS  Google Scholar 

  86. Quero M (1970) Atresia of the left atrioventricular orifice associated with a Holmes heart. Circulation 42: 739–744

    PubMed  CAS  Google Scholar 

  87. Quero M (1972) Coexistence of single ventricle with atresia of one atrioventricular orifice. Circulation 46: 794–798

    PubMed  CAS  Google Scholar 

  88. Rahimtoola SH, Ongley PA, Swan JC (1966) The hemodynamics of common (or single) ventricle. Circulation 34: 14–23

    PubMed  CAS  Google Scholar 

  89. Rao PS (1977) Natural history of the ventricular septal defect in tricuspid atresia and its surgical implications. Br Heart J 39: 276–288

    Article  PubMed  CAS  Google Scholar 

  90. Rao PS, Sissman NJ (1971) Spontaneous closure of physiologically advantageous ventricular septal defects. Circulation 43: 83–90

    PubMed  CAS  Google Scholar 

  91. Rao PS, Kulangara RJ, Moore V, Strong WB (1981) Syndrome of single ventricle without pulmonary stenosis but with left atrioventricular valve atresia and interatrial obstruction. Palliative management with simultaneous atrial septostomy and pulmonary artery banding. J Thorac Cardiovasc Surg 81: 127–130

    Google Scholar 

  92. Restivo A, Ho S, Anderson RH, Cameron H, Wilkinson JL (1982) Absent left atrioventricular connection with right atrium connected to morphologically left ventricular chamber, rudimentary right ventricular chamber, and ventriculoarterial discordance. Problem of mitral versus tricuspid atresia. Br Heart J 48: 240–248

    Article  PubMed  CAS  Google Scholar 

  93. Rice MJ, Seward JB, Edwards W et al. (1985) Straddling atrioventricular valve: two-dimensional echocardiographic diagnosis, classification and surgical implications. Am J Cardiol 55: 505–513

    Article  PubMed  CAS  Google Scholar 

  94. Rigby ML, Anderson RH, Gibson D, Jones OD, Joseph MC, Shinebourne EA (1981) Two-dimensional echocardiographic categorization of the univentricular heart: ventricular morphology, type and mode of atrioventricular connection. Br Heart J 46: 603–612

    Article  PubMed  CAS  Google Scholar 

  95. Rigby ML, Gibson DG, Joseph MC et al. (1982) Recognition of imperforate atrioventricular valves by two-dimensional echocardiography. Br Heart J 47: 329–336

    Article  PubMed  CAS  Google Scholar 

  96. Rosenquist G, Olney M, Roe BB (1963) The Holmes heart — a variant of cor triloculare biatrium. Report of case in a child. Circulation 27: 1143–1147

    Google Scholar 

  97. Rosenthal A, Freed MD, Fyler DC, Litwin SB (1974) Observations on the development of subaortic stenosis following pulmonary artery banding. Chest 65: 420–423

    Article  PubMed  CAS  Google Scholar 

  98. Rossi MB, Ho SY, Anderson RH (1986) Double inlet ventricle and its relationship to hearts with straddling and overriding atrioventricular valves. Rev Latina de Card Inf 3: 171–179

    Google Scholar 

  99. Rothman A, Lang P, Lock JE, Jonas RA, Mayer JE, Castaneda AR (1987) Surgical management of subaortic obstruction in single left ventricle and tricuspid atresia J Am Coll Cardiol 10: 421–426

    CAS  Google Scholar 

  100. Saalouke MG, Perry LW, Okoroma EO, Shapiro SR, Scott LPI (1978) Primitive ventricle with normally related great vessels and stenotic subpulmonary outlet chamber. Angiographic differentiation from tetralogy of Falot. Br Heart J 40: 49–54

    Google Scholar 

  101. Sahn DJ, Harder JR, Freedom RM et al. (1982) Cross-sectional echocardiographic diagnosis and sub-classification of univentricular hearts: imaging studies of atrioventricular valves, septal structures and rudimentary outflow chambers. Circulation 66: 1070–1077

    Article  PubMed  CAS  Google Scholar 

  102. Seliem M, Muster AJ, Paul MH, Benson DW Jr (1989) Relation between preoperative left ventricular muscle mass and outcome of the Fontan procedure in patients with tricuspid atresia. J Am Coll Cardiol 14: 750–755

    Article  PubMed  CAS  Google Scholar 

  103. Seward JB, Tajik AJ, Hagler DJ (1978) Echocardiographic spectrum of tricuspid atresia. Mayo Clin Proc 53: 100–112

    PubMed  CAS  Google Scholar 

  104. Shiraishi H, Silverman NH (1990) Echocardiographic spectrum of double inlet ventricle: evaluation of the interventricular communication. J Am Coll Cardiol 15: 1401–1408

    Article  PubMed  CAS  Google Scholar 

  105. Smallhorn JF, Tommasini G, Macartney FJ (1981) Detection and assessment of straddling and overriding atrioventricular valves by two-dimensional echocardiography. Br Heart J 46: 254–262

    Article  PubMed  CAS  Google Scholar 

  106. Smallhorn JF, Tommasini G, Macartney FJ (1981) Two-dimensional echocardiographic assessment of common atrioventricular valves in univentricular hearts. Br Heart J 46: 30–34

    Article  PubMed  CAS  Google Scholar 

  107. Smallhorn JF, Tommasini G, Anderson RH, Macartney FJ (1982) Assessment of atrioventricular septal defects by two-dimensional echocardiography. Br Heart J 47: 109–121

    Article  PubMed  CAS  Google Scholar 

  108. Somerville J (1979) Changing form and function in one ventricle hearts. Herz 4: 206–212

    PubMed  CAS  Google Scholar 

  109. Somerville J (1979) Congenital heart disease -changes in form and function. Br Heart J 41: 1–22

    Article  PubMed  CAS  Google Scholar 

  110. Somerville J, Becu L, Ross D (1974) Common ventricle with acquired subaortic obstruction. Am J Cardiol 34: 206–214

    Article  PubMed  CAS  Google Scholar 

  111. Somerville J, Ross DN, Yacoub M, Radley-Smith R (1975) Primitive ventricle with acquired subpulmonary stenosis. Eur J Cardiol 3: 193–203

    PubMed  CAS  Google Scholar 

  112. Soto B, Pacifico AD, Di Sciascio G (1982) Univentricular heart: an angiographic study. Am J Cardiol 49: 787–794

    Article  PubMed  CAS  Google Scholar 

  113. Stare TJ, Gersony WM (1986) Progressive obstruction of the foramen ovale in patients with left atrioventricular valve atresia. J Am Coll Cardiol 7: 1099–1103

    Article  Google Scholar 

  114. Sullivan ID, Taylor JFN (1989) Hearts with one ventricle: current concepts and management. Arch Dis Child 64: 166–171

    Article  PubMed  CAS  Google Scholar 

  115. Tandon R, Becker AE, Moller JH, Edwards JE (1974) Double inlet left ventricle. Straddling tricuspid valve. Br Heart J 36: 747–759

    Google Scholar 

  116. Taussig HB (1976) Long-term observations on the Blalock-Taussig operation, vol. 9. Single ventricle (with apex to the left). Johns Hopkins Med J 39: 69–76

    Google Scholar 

  117. Thies WR, Soto B, Diethelm E, Bargeron LMJ, Pacifico AD (1985) Angiographic anatomy of hearts with one ventricular chamber: the true single ventricle. Am J Cardiol 55: 1363–1366

    Article  PubMed  CAS  Google Scholar 

  118. Thies W-R, Bargeron LMJ, Bini RM, Colvin EV, Soto B (1986) Spectrum of hearts with one underdeveloped and one dominant ventricle. Pediatr Cardiol 7: 129–139

    Article  PubMed  CAS  Google Scholar 

  119. Trusler GA, Freedom RM (1989) Management of subaortic stenosis in the univentricular heart. Ann Thorac Surg 47: 643–645

    Article  PubMed  CAS  Google Scholar 

  120. Van Praagh R, Ongley PA, Swan HJC (1964) Anatomic types of single or common ventricle in man. Morphologic and geometric aspects of 60 necropsied cases. Am J Cardiol 13: 367–386

    Article  Google Scholar 

  121. Van Praagh R, Plett JA, Van Praagh S (1979) Single ventricle. Pathology, embryology, terminology and classification. Herz 4: 113–150

    Google Scholar 

  122. Van Praagh R, David I, Wright GB, Van Praagh S (1980) Large RV plus small LV is not a single RV (letter to the editor). Circulation 61: 1057

    PubMed  Google Scholar 

  123. Van Praagh R, David I, Van Praagh S (1982) What is a ventricle? The single ventricle trap. Pediatr Cardiol 2: 79–84

    Article  PubMed  Google Scholar 

  124. Waldman JD, Lamberti JL, George L et al. (1988) Experience with Damus procedure. Circulation 78 (Suppl III): 32–39

    Google Scholar 

  125. Weigel TJ, Driscoll DJ, Michels VV (1989) Occurrence of congenital heart defects in siblings of patients with univentricular heart and tricuspid atresia. Am J Cardiol 64: 768–771

    Article  PubMed  CAS  Google Scholar 

  126. Wilkinson JL, Becker AE, Tynan M et al. (1979) Nomenclature of the univentricular heart. Herz 4: 107–112

    PubMed  CAS  Google Scholar 

  127. Zuberbuhler JR (1989) Double-inlet ventricle. In: Moller JH, Neal WA (eds) Fetal, neonatal, and infant cardiac disease. Appleton and lange, Norwalk, Connecticut, pp 603–619

    Google Scholar 

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  1. R. M. Freedom
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  2. J. F. Smallhorn
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© 1992 Springer-Verlag London Limited

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Freedom, R.M., Smallhorn, J.F. (1992). Hearts with a Univentricular Atrioventricular Connection. In: Neonatal Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-1814-5_30

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  • DOI: https://doi.org/10.1007/978-1-4471-1814-5_30

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-1816-9

  • Online ISBN: 978-1-4471-1814-5

  • eBook Packages: Springer Book Archive

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