Abstract
Double-outlet ventricle refers to a heterogeneous group of cardiac lesions unified by an abnormal ventriculoarterial connection. This is not a diagnosis made on clinical grounds alone. Rather it is made by contemporary imaging techniques including cross-sectional echocardiography and angiocardiography. In this chapter we will explore the neonatal recognition and management of patients with those cardiac malformations sharing in common the abnormal ventriculoarterial connection of double-outlet right ventricle.
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References
Abe T, Sugiki K, Izumiyama O, Komatsu S (1984) A successful procedure for correction of the Taussig-Bing malformation. J Thorac Cardiovasc Surg 87: 403–409
Agarwala B, Doyle EF, Danilowicz D, Spencer FC, Mills NM (1973) Double-outlet right ventricle with pulmonic stenosis and anteriorly positioned aorta ( Taussig-Bing variant ). Am J Cardiol 32: 850–854
Ainger LE (1965) Double-outlet right ventricle: intact ventricular septum, mitral stenosis, and blind left ventricle. Am Heart J 70: 521–525
Anderson RH, Becker AE, Wilcox BR, Macartney FJ, Wilkinson JL (1983) Surgical anatomy of double-outlet right ventricle — a reappraisal. Am J Cardiol 52:555- 559
Aziz KU, Paul MH, Muster AJ, Idriss FS (1979) Positional abnormalities of atrioventricular valves in transposition of the great arteries including double- outlet right ventricle, atrioventricular valve straddling and malattachment. Am J Cardiol 44: 1135–1145
Baker WP, Kelminson LL, Turner Jr WM, Blount Jr SG (1967) Absence of pulmonic valve associated with double-outlet right ventricle. Circulation 36: 452–455
Baron MG (1971) Radiologic notes in cardiology — angiographic differentiation between tetralogy of Fallot and double-outlet right ventricle. Relationship of the mitral and aortic valves. Circulation 43: 451–455
Beuren A (1960) Differential diagnosis of the Taussig- Bing heart from complete transposition of the great vessels with a posteriorly overriding pulmonary artery. Circulation 21: 1071–1087
Bharati S, Lev M (1976) The conduction system in double-outlet right ventricle with subpulmonary ventricular septal defect and related hearts. Circulation 54: 459–467
Bharati S, Kirklin JW, McAllister Jr HA, Lev M (1980) The surgical anatomy of common atrioventricular orifice associated with tetralogy of Fallot, double-outlet right ventricle and complete regular transposition. Circulation 61: 1142–1149
Bical O, Hazan E, Lecompte Y et al. (1984) Anatomic correction of transposition of the great arteries associated with ventricular septal defect: midterm results in 50 patients. Circulation 70: 891–897
Blancquaert A, Defloor E, Bossaert L, Kunnen M, De Maegd M, Derom F (1973) Double-outlet right ventricle with L-malposition of great arteries, ventricular d-loop, and three fibrotic leaflets in a stenotic subpulomonary conus. Br Heart J 35: 770–773
Carey LS, Edwards JE (1965) Roentgenographic features in cases with origin of both great vessels from the right ventricle without pulmonary stenosis. AJR 93: 269–297
Ceithaml EL, Puga FJ, Danielson GK, McGoon DC, Ritter DG (1984) Results of the Damus-Stansel-Kaye procedure for transposition of the great arteries and for double-outlet right ventricle with subpulmonary ventricular septal defect. Ann Thorac Surg 38: 433–437
Ciaravella Jr JM, McGoon DC, Hagler DJ, Fulton RE (1979) Caplike double-horned double-outlet right ventricle. J Thorac Cardiovasc Surg 77: 536–542
Damus PS, Thomson Jr NB, McLoughlin TG (1982) Arterial repair without coronary relocation for complete transposition of the great vessels with ventricular septal defect. J Thorac Cardiovasc Surg 83: 316–318
Danielson GK, Ritter DG, Coleman HNI, Du Shane JW (1972) Successful repair of double-outlet right ventricle with transposition of the great arteries (aorta anterior and to the left) pulmonary stenosis, and subaortic ventricular septal defect. J Thorac Cardiovasc Surg 63: 741–746
Danielson GK, Tabry IF, Mair DD, Fulton RE (1978) Great-vessel switch operation without coronary relocation for transposition of great arteries. Mayo Clin Proc 53: 675–682
De La Cruz MV, Espino-Val J, Alarcon AV, Gomez CS, Trevino CP (1986) Double outlet right ventricle. Anatomo-embryological classification with angiographic and surgical considerations. II Cuore III: 25–37
De Leon SY, Idriss FS, Ilbawi MN et al. (1986) The Damus-Stansel-Kaye procedure. Should the aortic valve or subaortic valve region be closed? J Thorac Cardiovasc Surg 91: 747–753
De Tommasi SM, Daliento L, Ho SY, Macartney FJ, Anderson RH (1981) Analysis of atrioventricular junction, ventricular mass and ventriculo-arterial junction in 43 specimens with atrial isomerism. Br Heart J 45: 236–247
Deutsch V, Shem-Tov A, Yahini JH, Neufeld HN (1970) Cardioangiographic evaluation of the relationship between atrioventricular and semilunar valves: its diagnostic importance in congenital heart disease. AJR 110: 474–490
Edwards WD (1981) Double-outlet right ventricle and tetralogy of Fallot. Two distinct but not mutually exclusive entities. J Thorac Cardiovasc Surg 82:418- 422
Ettinger PO, Weisse AB, Khan MI, Levinson GE (1969) Double-outlet right ventricle in an adult with aortic regurgitation. Am J Med. 47: 818–824
Ferencz C, Rubin JD, McCarter RJ (1985) Congenital heart disease: prevalence at livebirth. The Baltimore- Washington infant study. Am J Epidemiol 121: 31–36
Freedom RM, Bini R, Dische R, Rowe RD (1978) The straddling mitral valve: morphological observations and clinical implications. Euro J Cardiol 8: 27–50
Freedom RM, Culham G, Rowe RD (1978) The crisscross and superoinferior ventricular heart: an angiocardiographic study. Am J Cardiol 42: 620–628
Freedom RM, Culham JAG, Moes CAF (1984) Angiocardiography of congenital heart disease. Macmillan, New York, pp 555–574
Freedom RM, Smallhorn JF (1989) Double-outlet ventricle. In: Moller JH, Neal WA (eds) Fetal, neonatal, and infant cardiac disease. Appleton and Lange, Norwalk, Connecticut, pp 621–637
Fyler DC (1980) Report of the New England regional infant cardiac program. Pediatrics 65 (Suppl): 376–461
Gerlis LM, Dickinson DF, Anderson RH (1984) Dis-advantageous closure of the interventricular communication in double-outlet right ventricle. Br Heart J 51: 670–673
Golan M, Hegesh J, Massini C, Goor DA (1984) Double-outlet right ventricle associated with subaortic stenosis. Pediatr Cardiol 5: 157–158
Gomes MMR, Weidman WH, McGoon DC, Danielson GK (1971) Double-outlet right ventricle with pulmonic stenosis, surgical considerations and results of operation. Circulation 43: 889–894
Goor DA Ebert PA (1975) Left ventricular outflow obstruction in Taussig-Bing malformation. Anatomic and surgical implications. J Thorac Cardiovasc Surg 70: 69–75
Hagler DJ, Tajik AJ, Seward JB, Mair DD, Ritter DG (1981) Double-outlet right ventricle: wide-angle two-dimensional echocardiographic observations. Circulation 63: 419–428
Hagler DJ, Ritter DG, Puga FJ (1989) Double-outlet right ventricle. In: Adams FH, Emmanouilides GC, Riemenschneider TA (eds) Moss’ heart disease in infants, children, and adolescents. Williams and Wilkins, Baltimore, pp 442–460
Hallermann FJ, Kincaid OW, Ritter DG, Ongley PA, Titus JL (1970) Angiocardiographic and anatomic findings in origin of both great arteries from the right ventricle. AJR 109: 51–66
Harvey JC, Sondheimer HM, Williams WG, Olley PM, Trusler GA (1977) Repair of double-outlet right ventricle. J Thorac Cardiovasc Surg 73: 611–615
Henry WL, Maron BJ, Griffith JM (1977) Cross-sectional echocardiography in the diagnosis of congenital heart disease. Identification of the relation of the ventricles and great arteries. Circulation 56:267- 273
Hightower BM, Barcia A, Bargeron LM Jr, Kirklin JW (1969) Double-outlet right ventricle with transposed great arteries and subpulmonary ventricular septal defect: the Taussig-Bing malformation. Circulation 39 and 40 (Suppl I): 207–213
Hinkes P, Rosenquist GC, White Jr RI (1971) Roentgenographic re-examination of the internal anatomy of the Taussig-Bing heart. Am Heart J 81: 335–339
Huhta JC, Edwards WD, Danielson GK, Feldt RH (1982) Abnormalities of the tricuspid valve in complete transposition of the great arteries with ventricular septal defect. J Thorac Cardiovasc Surg 83: 569–576
Judson JP, Danielson GK, Puga FJ, Mair DD, McGoon DC (1983) Double-outlet right ventricle. Surgical results 1970–1980. J Thorac Cardiovascular Surg 85:32- 40
Kanter K, Anderson R, Liincoln C, Firmin R, Rigby M (1986) Anatomic correction of double-outlet right ventricle with subpulmonary ventricular septal defect (the Taussig-Bing anomaly). Ann Thorac Surg 41: 287–292
Kawashima Y, Fugita T, Miyamoto T, Manabe H (1971) Intraventricular re-routing of blood for the correction of Taussig-Bing malformation. J Thorac Cardiovasc Surg 62: 825–829
Kirklin JW, Barratt-Boyes BG (1986) Cardiac surgery. Wiley, New York, pp 1219–1250
Kirklin JK, Castaneda AR (1977) Surgical correction of double-outlet right ventricle with non-committed ventricular septal defect. J Thorac Cardiovasc Surg 73:399- 403
Kirklin JW, Harp RA, McGoon DC (1964) Surgical treatment of origin of both vessels from right ventricle, including cases of pulmonary stenosis. J Thorac Cardiovasc Surg 48: 1024–1036
Kitamura N, Takao A, Ando M, Imai Y, Konno S (1974) Taussig-Bing heart with mitral valve straddling. Case reports and postmortem study. Circulation 49: 761–767
Krongrad E, Ritter DG, Weidman WH, Du Shane JE (1972) Hemodynamic and anatomic correlation of electrocardiogram in double-outlet right ventricle. Circulation 46: 995–1004
Kurosawa H, Van Mierop LHS (1986) Surgical anatomy of the infundibular septum in transposition of the great arteries with ventricular septal defect. J Thorac Cardiovasc Surg 91: 123–132
Kurosawa H, Imai Y, Takanashi Y et al. (1986) Infundibular septum and coronary anatomy in Jatene operation. J Thorac Cardiovasc Surg 91: 572–583
Lavoie R, Sestier F, Gilbert G, Chameides L, Van Praagh R, Grondin P (1971) Double-outlet right ventricle with left ventricular outflow tract obstruction due to a small ventricular septal defect. Am Heart J 82:290- 299
Lev M, Bharati S (1973) Double-outlet right ventricle- association with other cardiovascular anomalies. Arch Pathol 95: 117–122
Lev M, Rimoldi HJA, Eckner FAO, Melhuish BP, Meng L, Paul MH. (1966) The Taussig-Bing heart. Arch Pathol 81: 24–35
Lev M, Bharati S, Meng CCL, Liberthson RR, Paul MH, Idriss F (1972) A concept of double-outlet right ventricle. J Thorac Cardiovasc Surg 64: 271–281
Lincoln C, Anderson RH, Shinebourne EA, English TAH, Wilkinson JL. (1975). Double-outlet right ventricle with L-malposition of the aorta. Br Heart J 37:453–463
Macartney FJ, Rigby ML, Anderson RH, Stark J, Silverman NH (1984) Double-outlet right ventricle. Cross-sectional echocardiographic findings, their anatomical explanation, and surgical relevance. Br Heart J 52: 164–177
MacMahon HE, Lipa M (1964) Double-outlet right ventricle with intact interventricular septum. Circulation 30: 745–748
Marin-Garcia J, Neches WH, Park SC, Lenox CC, Zuberbuhler JR, Bahnson HT (1978) Double-outlet right ventricle with restrictive ventricular septal defect. J Thorac Cardiovasc Surg 76: 853–858
Marino B, Loperfido F, Sardi CS (1983) Spontaneous closure of ventricular septal defect in a case of double-outlet right ventricle. Br Heart J 49: 608–611
Mazzuco A, Faggion G, Stellin GEA (1985) Surgical management of double-outlet right ventricle. J Thorac Cardiovasc Surg 90: 29–34
Megarity AL, Chambers RD, Calder AL, Van Praagh S, Van Praagh R (1972) Double-outlet right ventricle with left ventricular-right atrial communication: fibrous obstruction of left ventricular outlet by membranous septum and tricuspid leaflet tissue. Am Heart J 84: 242–249
Milo S, Ho SY, Wilkinson JL, Anderson RH (1980) The surgical anatomy and atrioventricular conduction tissues of hearts with isolated ventricular septal defects. J Thorac Cardiovasc Surg 79: 244–255
Mirowski M, Mehrizi A, Taussig HB (1963) The electrocardiogram in patients with both great vessels arising from the right ventricle combined with pulmonary stenosis. Circulation 28: 1116–1127
Misra KP, Cohen LS (1971) Double-outlet right ventricle with origin of right pulmonary artery from a right-sided ductus arteriosus. Am Heart J 82: 228–231
Muster AJ, Bharati S, Aziz KU (1979) Taussig-Bing anomaly with straddling mitral valve. J Thorac Cardiovasc Surg 77: 832–842
Nadas AS, Fyler DC (1972) Pediatric cardiology. Saunders, New York, pp 638–640
Neufeld HN, Du Shane JW, Wood EH, Kirklin JW, Edwards JE (1961) Origin of both great vessels from the right ventricle. I. Without pulmonary stenosis. Circulation 23: 399–412
Neufeld HN, Du Shane JW, Edwards JE (1961) Origin of both great vessels from the right ventricle. II. With pulmonary stenosis. Circulation 23: 603–612
Neufeld HN, Lucas Jr RV, Lester RG, Adams Jr P, Anderson RC, Edwards JE (1962) Origin of both great vessels from the right ventricle without pulmonary stenosis. Br Heart J 24: 393–408
Otero-Coto E, Jimenez MQ, Cabrera A, Deverall PB, Caffarena JM (1978) Aortic levopositions without ventricular inversion. Eur J Cardiol 8: 523–541
Pacifico AD, Stewart RW, Bargeron Jr LM (1983) Repair of transposition of the great arteries with ventricular septal defect by an arterial switch operation. Circulation 68 (Suppl II): 49–55
Parr GVS, Waldhausen JA, Bharati S, Lev M, Fripp R, Whitman V (1983) Coarctation in Taussig-Bing malformation of the heart. J Thorac Cardiovasc Surg 86: 280–287
Patrick DL, McGoon DC (1968) Operation for double- outlet right ventricle with transposition of the great arteries. J Cardiovasc Surg 19: 537–542
Pellegrino PA, Eckner FA, Meier MA, Lev M (1973) Double-outlet right ventricle with fibromuscular obstruction to left ventricular outlet. J Cardiovasc Surg 14: 253–260
Penkoske PA, Westerman GR, Marx GR et al. (1983) Transposition of the great arteries and ventricular septal defect: results with the Senning operation and closure of the ventricular septal defect in infants. Ann Thorac Surg 36: 281–288
Piccoli G, Pacifico AD, Kirklin JW, Blackstone EH, Kirklin JK, Bargeron LM (1983) Changing results and concepts in the surgical treatment of double-outlet right ventricle: analysis of 137 operations in 126 patients. Am J Cardiol 52: 549–554
Quaegebeur JM (1983) The optimal repair for the Taussig-Bing heart. J Thorac Cardiovasc Surg 85:276- 277
Rice MJ, Seward JB, Edwards WD (1985) Straddling atrioventricular valve: two-dimensional echocardiographic diagnosis, classification and surgical implications. Am J Cardiol 55: 505–513
Rowe RD, Freedom RM, Mehrizi A (1981) The neonate with congenital heart disease. Saunders, New York, pp 309–327
Russo P, Danielson GK, Puga FJ, McGoon DC, Humes R (1988) Modified Fontan procedure for biventricular hearts with complex forms of double-outlet right ventricle. Circulation 78 (Suppl III): 20–25
Ruttenberg HD, Anderson RC, Elliott LP, Edwards JE (1964) Origin of both great vessels from the arterial ventricle: a complex with ventricular inversion. Br Heart J 26: 631–641
Sadow SH, Synhorst DP, Pappas G (1985) Taussig- Bing anomaly and coarctation of the aorta in infancy: surgical options. Pediatr Cardiol 6: 83–90
Sanders SP, Bierman FZ, Williams RG (1982) Con- otruncal malformations: diagnosis in infancy using subxiphoid 2-dimensional echocardiography. Am J Cardiol 50: 1361–1367
Serratto M, Arevalo F, Goldman EJ, Hastreiter A, Miller RA (1967) Obstructive ventricular septal defect in double-outlet right ventricle. Am J Cardiol 19: 457–463
Smallhorn JF, Tommasini G, Macartney FJ (1981) Detection and assessment of straddling and overriding atrioventricular valves by two-dimensional echocardiography. Br Heart J 46: 254–262
Smith EEJ, Pucci JJ, Walesby RK, Oakley CM, Sapsford RN (1982) A new technique for correction of the Taussig-Bing anomaly. J Thorac Cardiovasc Surg 83: 901–904
Smolinsky A, Castaneda AR, Van Praagh R (1988) Infundibular septal resection: surgical anatomy of the superior approach. J Thorac Cardiovasc Surg 95:486- 494
Snoddy JW, Parr EL, Robertson LW, Mauck Jr HP, McCue CM, Lower RR (1978) Successful intracardiac repair of the Taussig-Bing malformation in 2 children. Ann Thorac Surg 25: 158–163
Sondheimer HM, Freedom RM, Olley PM (1977) Double-outlet right ventricle: clinical spectrum and prognosis. Am J Cardiol 39: 709–714
Sondheimer HM, Freedom RM, Olley PM (1978) Double-outlet right ventricle. In: Keith JD, Rowe RD, Vlad P (eds) Heart disease in infancy and childhood. Macmillan, New York, pp 628–637
Sridaromont S, Feldt RH, Ritter DG, Davis GD, Edwards JE (1975) Double-outlet right ventricle associated with persistent common atrioventricular canal. Circulation 52: 933–942
Sridaromont S, Feldt RH, Ritter DG, David GD, Edwards JE (1976) Double-outlet right ventricle, hemodynamic and anatomic correlations. Am J Cardiol 28: 85–94
Sridaromont S, Ritter DG, Feldt RH, Davis GD, McGoon DC, Edwards JE (1978) Double-outlet right ventricle. Anatomic and angiographic correlations. Mayo Clin Proc 53: 556–563
Tandon R, Moller JH, Edwards JE (1973) Communication of mitral valve with both ventricles associated with double-outlet right ventricle. Circulation 48: 904–908
Taussig HB, Bing RJ (1949) Complete transposition of the great arteries and a levoposition of the pulmonary artery. Am Heart J 37: 551–557
Thanopoulos BD, Dubrow IW, Fisher EA, Hastreiter AR (1979) Double-outlet right ventricle with subvalvu- lar aortic stenosis. Br Heart J 41: 241–244
Toews WH, Lortscher RH, Kelminson LL (1975) Double-outlet right ventricle with absent aortic valve. Chest 68: 381–382
Tynan MJ, Becker AE, Macartney FJ, Quero-Jimenez M, Shinebourne EA, Anderson RH (1979) Nomenclature and classification of congenital heart disease. Br Heart J 41: 544–553
Van Praagh R (1968) What is the Taussig-Bing malformation? Circulation 38: 445–449
Van Praagh R (1973) Conotruncal malformations. In: Barratt-Boyes BG, Neutze JM, Havis EA (eds) Heart disease in infancy: diagnosis and surgical treatment. Churchill Livingstone, Edinburgh, pp 140–188
Van Praagh S, Dick M, Delisle G, Van Praagh R (1973) Ventricule droit a double issue. Constatations necropsiques sur 45 cas et applications diagnostiques et chirurgicales. Coeur (Numero Speciale) 319–321
Van Praagh R, Perez-Trevino C, Reynolds JL (1975) Double-outlet right ventricle SDL with subaortic ventricular septal defect and pulmonary stenosis. Am J Cardiol 35: 42–53
Waldman JD, Lamberti JL, George L (1988) Experience with Damus procedure. Circulation 78 (Suppl. 3): 32- 39
Wedemeyer AL, Lucas Jr RV, Castaneda AR (1970) Taussig-Bing malformation, coarctation of the aorta, and reversed patent ductus arteriosus. Operative correction in an infant. Circulation 42: 1021–1027
Weir EK, Joffe HS, Barnard CN, Beck W (1978) Double-outlet right ventricle: clinical and anatomical spectrum. Thorax 33: 283–289
Wilkinson JL (1987) Double-outlet ventricle. In: Anderson RH, Macartney FJ, Shinebourne EA, Tynan M (eds) Paediatric cardiology. Churchill Livingstone, Edinburgh, pp 889–911
Wilkinson JL, Wilcox BN, Anderson RH (1983) The anatomy of double-outlet right ventricle. In: Anderson RH, Macartney FJ, Shinebourne EA, Tynan M (eds) Paediatric cardiology. Churchill Livingstone, Edinburgh, pp 397–407
Yacoub MH, Radley-Smith R (1984) Anatomic correction of the Taussig-Bing anomaly. J Thorac Cardiovasc Surg 88: 380–388
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Freedom, R.M., Smallhorn, J.F. (1992). Double-Outlet Right Ventricle. In: Neonatal Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-1814-5_27
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