Tricuspid Atresia

  • R. M. Freedom
  • L. N. Benson


It is likely that the natural history, indeed the fortunes, of the patient with tricuspid atresia, was irrevocably altered by the surgical innovation of Fontan and Baudet of Bordeaux, who in 1971 reported the construction of an atriopulmonary anastomosis with atrial partitioning as a means of separating the systemic venous from the pulmonary venous circulations in children with tricuspid atresia [21]. Indeed, surgical history was made by this ingenious contribution, and in the next nearly two decades this procedure, or one of its many technical modifications, has been extended to almost every form of congenitally malformed heart where anatomical constraints prevent a biventricular repair (see Chapter 30) [15,16, 22, 37, 38, 39, 40, 41, 43, 49, 64, 68]. The management of the neonate with tricuspid atresia is to preserve the integrity of the myocardium and pulmonary vascular bed for Fontan’s operation.


Ventricular Septal Defect Pulmonary Blood Flow Interatrial Communication Pulmonary Artery Banding Tricuspid Atresia 
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© Springer-Verlag London Limited 1992

Authors and Affiliations

  • R. M. Freedom
  • L. N. Benson

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