Clinical Perspective: Electrophysiology in the Young and Patients with Congenital Heart Disease

  • James C. Perry


Young patients and those with congenital heart disease (CHD) manifest all forms of cardiac arrhythmia, but the age of presentation varies considerably, and the indications for intervention differ from adults. Much remains to be discovered about the underlying mechanisms of pediatric and congenital heart arrhythmia and even more about the true indications and benefits of pacemaker, defibrillator, and resynchronization device management strategies. The purpose of this chapter is to review the age-dependent presentation of cardiac arrhythmias, their relation to structural congenital cardiac defects, and the growing implication of the needs of the adult population with CHD for improved heart failure and primary prevention guidelines.


Congenital Heart Disease Right Ventricle Cardiac Resynchronization Therapy Right Bundle Branch Block Implantable Cardiac Defibrillator 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.



antiarrhythmic drug




congenitally corrected transposition of the great arteries


congenital heart disease


cardiac resynchronization therapy


d-transposition of the great arteries




implantable cardioverter-defibrillator


right bundle branch block


single nucleotide polymorphism


supraventricular tachycardia


tetralogy of Fallot


ventricular septal defect


ventricular tachycardia


Wolff–Parkinson–White syndrome


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Copyright information

© Springer Science+Business Media, LLC 2010

Authors and Affiliations

  1. 1.Department of Pediatrics, Cardiology DivisionUniversity of California San Diego/Rady Children’s HospitalSan DiegoUSA

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