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The Sclera pp 277-297 | Cite as

Noninflammatory Diseases of the Sclera

  • Maite Sainz de la Maza
  • Joseph Tauber
  • C. Stephen Foster
Chapter

Abstract

Like scleritis and episcleritis, noninflammatory diseases of the sclera cannot be properly understood as isolated entities but must be seen in relation to the larger picture of a patient´s general health. Noninflammatory affections of the sclera may be manifestations of ocular diseases, such as the connective tissue abnormalities, degenerations, or tumors. They also may be signs of systemic diseases, such as metabolic disorders, connective tissue abnormalities, or hematologic disorders. In many cases, the characteristics of the scleral abnormality (deposit, thinning, thickening, or mass) are sufficiently distinctive that the ocular or systemic diagnosis is first suspected by the ocular presentation. Ophthalmologists must be competent enough to recognize this interconnection and therefore, promptly diagnose and, if possible, treat the underlying ocular or systemic disease.

Keywords

Osteogenesis Imperfecta Porphyria Cutanea Tarda Homogentisic Acid Angioid Streak Pseudoxanthoma Elasticum 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Maite Sainz de la Maza
    • 1
  • Joseph Tauber
    • 2
  • C. Stephen Foster
    • 3
  1. 1.Clinical Institute of OphthalmologyHospital Clinic of BarcelonaBarcelonaSpain
  2. 2.Tauber Eye CenterKansas CityUSA
  3. 3.Massachusetts Eye Research and Surgery InstitutionCambridgeUSA

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