Abnormal Venous Drainage

  • Sanjay P. Prabhu
  • Edward Y. Lee
  • Annabelle Quizon


Congenital pulmonary venous anomalies, which arise from abnormal embryonic venous development, occur in a diverse spectrum in the pediatric population. Although echocardiography with pulsed Doppler remains the initial investigation of choice in evaluation of the pulmonary venous developmental anomalies particularly in infants and young children, noninvasive imaging studies such as Magnetic Resonance Imaging and Multidetector Computed Tomography are currently playing increasing roles in the initial diagnosis and further characterization of this group of disorders. In this chapter, we review (1) embryology; (2) epidemiology; (3) anatomy; (4) clinical presentation; (5) preoperative imaging evaluation; (6) management; and (7) postoperative imaging evaluation of congenital pulmonary venous anomalies in the pediatric population. Disorders of the lymphatic system encompass a number of entities that may lead to chronic and serious pulmonary disease and manifest with a range of clinical presentations. Congenital errors in lymphatic development are rare and their diagnoses and management are difficult.


Pulmonary Vein Left Atrium Pulmonary Vein Stenosis Total Anomalous Pulmonary Venous Connection Pulmonary Venous Obstruction 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Sanjay P. Prabhu
    • 1
  • Edward Y. Lee
    • 2
  • Annabelle Quizon
    • 3
  1. 1.Department of RadiologyChildren’s Hospital Boston and Harvard Medical SchoolBostonUSA
  2. 2.Division of Thoracic Imaging, Department of Radiology and Medicine, Pulmonary DivisionChildren’s Hospital BostonBostonUSA
  3. 3.Department of Pediatrics, Division of Pediatric PulmonologyUniversity of Miami/Miller School of Medicine, Batchelor Children’s Research InstituteMiamiUSA

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