Congenital Portosystemic Shunts: Diagnosis and Percutaneous Management



Congenital portosystemic shunts, first described in 1793 by London surgeon John Abernethy, are rare congenital communications between the portal and the systemic venous system. These shunts are caused by the anomalous development of the hepatic vasculature during the embryologic period. Congenital absence of the portal vein is thought to arise due to an early involution of the periduodenal vitelline veins. Shunts between the right portal vein and systemic systems are thought to arise due to persistence of the right vitelline vein. Shunts between the left portal vein and systemic circulation are thought to be due to persistence of the left vitelline vein.


Portal Hypertension Biliary Atresia Choledochal Cyst Hepatopulmonary Syndrome Shunt Ratio 
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© Springer Science+Business Media New York 2014

Authors and Affiliations

  1. 1.Interventional RadiologyIndiana University School of Medicine, Riley Hospital for ChildrenIndianapolisUSA
  2. 2.Department of RadiologyIndiana University School of MedicineIndianapolisUSA

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