The presacral or retrorectal space may be the site of a group of heterogeneous and rare tumors that display indolent growth and produce ill-defined symptoms. As detection is often difficult and delayed, patients frequently present with tumors that have reached considerable size and involve multiple organ systems, complicating their treatment. The diagnosis and management of these tumors has evolved in recent years due to improved imaging modalities, a better understanding of tumor biology, adjuvant chemoradiation therapy and a more aggressive surgical approach. Few surgeons have the opportunity to treat these complex lesions, and the care of these patients can be greatly optimized by an experienced, multidisciplinary team.
KeywordsMalignant Peripheral Nerve Sheath Tumor Giant Cell Tumor Dermoid Cyst Preoperative Biopsy Presacral Space
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