Neurocognition in Mitochondrial Disorders

  • Kevin M. Antshel


A mitochondrion (plural mitochondria) is a specialized cellular subunit found in most living cells. Mitochondria generate most of a cell’s supply of adenosine triphosphate (ATP) and supply the cell with energy primarily derived from oxidation of carbohydrates and fatty acids in the mitochondria. A mitochondrion has its own DNA and its own transcription and translation processes. The mitochondrial DNA encodes only 13 polypeptides which are located in the inner mitochondrial membrane as subunits of the respiratory chain complexes.


Apparent Diffusion Coefficient Sensorineural Hearing Loss Mitochondrial Disease Mitochondrial Disorder Leigh Syndrome 
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© Springer Science+Business Media, LLC 2010

Authors and Affiliations

  1. 1.Department of Psychiatry and Behavioral SciencesState University of New York – Upstate Medical UniversitySyracuseUSA

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