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Pheochromocytoma and Paraganglioma

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Endocrine Neoplasia

Part of the book series: Cancer Treatment and Research ((CTAR,volume 153))

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Abstract

Pheochromocytomas and extra-adrenal sympathetic paragangliomas are catecholamine-secreting neuroendocrine tumors derived from the chromaffin cells of the embryonic neural crest. Parasympathetic paragangliomas are related tumors which most often arise within the head and neck, and are anatomically associated with the parasympathetic nervous system. Patients with pheochromocytomas and extra-adrenal sympathetic paragangliomas generally present with symptoms resulting from excessive production and secretion of catecholamines whereas parasympathetic paragangliomas usually present as a solitary and progressively enlarging mass without catecholamine secretion.

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Authors and Affiliations

  1. Department of Endocrine and Oncology Surgery, Royal North Shore Hospital, St Leonards, NSW, 2065, Australia

    Stan B. Sidhu

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  1. Goswin Y. Meyer-Rochow
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  2. Stan B. Sidhu
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Correspondence to Stan B. Sidhu .

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  1. Feinberg School of Medicine, Northwestern University, E. Huron St. 201, Chicago, 60611, U.S.A.

    Cord Sturgeon

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Meyer-Rochow, G.Y., Sidhu, S.B. (2010). Pheochromocytoma and Paraganglioma. In: Sturgeon, C. (eds) Endocrine Neoplasia. Cancer Treatment and Research, vol 153. Springer, Boston, MA. https://doi.org/10.1007/978-1-4419-0857-5_9

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