Visual Perceptual Effects of Long-Standing Vision Loss



This chapter focuses on the changes in vision experienced by patients with RP and AMD. The specific aspects of vision that are reviewed include progressive changes in central acuity, contrast sensitivity, visual field, color vision, night vision, glare, and light and dark adaptation. Emphasis is on patients’ perspectives, including the impact on functioning and performance of activities of daily living, as well as rates, patterns of vision loss, and day-to-day visual fluctuations experienced by those with retinal degenerative diseases. Several types of visual phenomena are presented, including Charles Bonnet Syndrome hallucinations in AMD, perceptual completion or filling-in of scotomas in AMD, remapping visual cortex in AMD, the preferred retinal locus in AMD, and photopsias or light show type flashes in RP. The proposed implications of these visual changes and phenomena as they apply to retinal prosthetic vision are discussed.


Visual Hallucination Visual Field Loss Punctate Inner Choroidopathy Charles Bonnet Syndrome Acute Zonal Occult Outer Retinopathy 



Acute idiopathic blind spot enlargement


Age-related macular degeneration


Acute zonal occult outer retinopathy


Charles Bonnet syndrome


Functional magnetic resonance imaging


Geographic atrophy


Multiple evanescent white dot syndrome


Punctate inner choroidopathy


Preferred retinal locus


Retinitis pigmentosa


Vascular endothelial growth factor


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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  1. 1.Lions Vision Research & Rehabilitation Center, Wilmer Eye InstituteJohns Hopkins University School of MedicineBaltimoreUSA

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