Neurofibromatosis: Tumors of the Optic Pathway

Chapter
Part of the M.D. Anderson Solid Tumor Oncology Series book series (MDA, volume 6)

Abstract

Various tumors occur in patients with neurofibromatosis type 1. In this chapter, we discuss the clinical presentation and evaluation of four types of tumors affecting patients with neurofibromatosis type 1: periorbital and orbital neurofibroma, intraorbital optic nerve glioma, chiasmal and hypothalamic glioma, and intraparenchymal astrocytoma. Treatment options are also discussed.

Keywords

Glaucoma Meningioma Hydrocephalus Astrocytoma Acetazolamide 

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Copyright information

© Springer Science+Business Media, LLC 2010

Authors and Affiliations

  1. 1.Department of Neuro-OncologyThe University of Texas M.D. Anderson Cancer CenterHoustonUSA
  2. 2.Section of Ophthalmology, Department of Head and Neck SurgeryThe University of Texas M.D. Anderson Cancer CenterHoustonUSA

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