Indian Childhood Cirrhosis and Other Metabolic Liver Diseases

  • Ashish Bavdekar
  • Stuart Tanner


Most paediatric centres in India serve a large population with a high rate of consanguinity. They may therefore expect to see many children with recessive genetic disorders, including metabolic liver disease. Even if individual conditions are rare, the total number of “metabolic” cases in a liver service will be substantial. They pose a major diagnostic challenge. They have to be distinguished from the larger group of children with infectious diseases or problems of malnutrition. Diagnostic facilities may be limited. They may also be seen as a lower priority than other more pressing paediatric problems, particularly if there is a perception that treatment is expensive or ineffective. Nevertheless, there are important reasons for recognising and attempting to diagnose and treat this group of children.


Acute Liver Failure Glycogen Storage Disease Glycogen Storage Disease Type Urea Cycle Disorder Indian Childhood Cirrhosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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© Springer Science+Business Media Dordrecht 2004

Authors and Affiliations

  • Ashish Bavdekar
  • Stuart Tanner

There are no affiliations available

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