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Anesthesia for Adult Congenital Aortic Surgery

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Anesthesia and Perioperative Care for Aortic Surgery

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Abstract

Congenital supravalvular aortic stenosis (SVAS) is a rare form of left ventricular outflow tract (LVOT) obstruction that often is associated with peripheral pulmonary artery stenoses (approximately 40% of patients). Congenital SVAS is an elastin ­arteriopathy and is most commonly associated with Williams–Beuren syndrome. Williams–Beuren syndrome, commonly referred to as Williams syndrome (WS), is characterized by the presence of SVAS and peripheral pulmonary artery stenoses in association with mental retardation and distinctive elfin facies.

This chapter is intended to be an overview of the anesthetic implications of those unrepaired ­congenital aortic lesions that are likely to be encountered in an adult population.

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Authors and Affiliations

  1. Department of Anesthesiology, Perioperative and Pain Medicine, Children’s Hospital Boston and Harvard Medical School, 300 Longwood Avenue, Boston, MA, USA

    Barry D. Kussman

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  1. Barry D. Kussman
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  2. James A. DiNardo
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Correspondence to Barry D. Kussman .

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Editors and Affiliations

  1. University of Pittsburgh Medical Center, Presbyterian Hospital, Clinical Assistant Professor, Pittsburgh, 15213-2582, Pennsylvania, USA

    Kathirvel Subramaniam

  2. Physician Director of Perioperative Serv, Professor of Clinical Anesthesia and of, Associate Vice President, Columbus, 43210, Ohio, USA

    Kyung W. Park

  3. Harvard Medical School, Director, Division of Cardiovascular Ane, Assistant Professor in Anesthesia, Boston, 02215, Massachusetts, USA

    Balachundhar Subramaniam

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Kussman, B.D., DiNardo, J.A. (2011). Anesthesia for Adult Congenital Aortic Surgery. In: Subramaniam, K., Park, K., Subramaniam, B. (eds) Anesthesia and Perioperative Care for Aortic Surgery. Springer, New York, NY. https://doi.org/10.1007/978-0-387-85922-4_17

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  • DOI: https://doi.org/10.1007/978-0-387-85922-4_17

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