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Adrenocortical Carcinoma pp 467–481Cite as

Adrenocortical Cancer in Children

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Abstract

Adrenocortical cancer (ACC) is a rare but aggressive childhood endocrine neoplasm. Its incidence in children is extremely low (only 0.2% of pediatric cancers) [1], and most pediatric oncologists see few cases or none. Little is known about this malignancy and most available information has been learned from its more frequent adult counterpart. In recent years, an international registry has provided insight into the clinical characteristics and relevant management issues regarding pediatric ACC and tumor tissue for biological studies. These studies have resulted in the discovery of a novel mechanism of tumorigenesis [2], the gift to science by one of the rarest childhood cancers.

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Author information

Authors and Affiliations

  1. Department of Pediatric Oncology, Dana-Farber Cancer Institute and Children’s Hospital, 44 Binney Street, Boston, MA, 02115, USA

    Carlos Rodriguez-Galindo

  2. Department of Biochemistry, St. Jude Children’s Research Hospital, 262 Danny Thomas Place, Memphis, TN, 38105, USA

    Gerard P. Zambetti

  3. Department of Oncology, St. Jude Children’s Research Hospital, 262 Danny Thomas Place, Memphis, TN, 38105, USA

    Raul C. Ribeiro

Authors
  1. Carlos Rodriguez-Galindo
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  2. Gerard P. Zambetti
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  3. Raul C. Ribeiro
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Corresponding author

Correspondence to Carlos Rodriguez-Galindo .

Editor information

Editors and Affiliations

  1. Zina Pitcher Place 109, Ann Arbor, 48109-2200, Michigan, USA

    Gary D. Hammer

  2. Dept. Internal Medicine, Div. Pulmonary & Critical Care Medicine, University of Michigan Health System, Zina Pitcher Place 109, Ann Arbor, 48109-2200, Michigan, USA

    Tobias Else

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Rodriguez-Galindo, C., Zambetti, G.P., Ribeiro, R.C. (2009). Adrenocortical Cancer in Children. In: Hammer, G., Else, T. (eds) Adrenocortical Carcinoma. Springer, New York, NY. https://doi.org/10.1007/978-0-387-77236-3_28

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