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Hereditary Optic Neuropathies

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Abstract

Leber’s hereditary optic neuropathy (LHON) is a painless, bilateral, acute or subacute optic neuropathy that is maternally inherited from mutations in the mitochondrial DNA. The exact worldwide incidence of LHON is unknown, but it is much less prevalent than other optic nerve disorders, such as optic neuritis and ischemic optic neuropathy. Men are affected two to three times more frequently than women.1-3

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    Jane W. Chan MD (Assciate Professor)

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Chan, J.W. (2007). Hereditary Optic Neuropathies. In: Optic Nerve Disorders. Springer, New York, NY. https://doi.org/10.1007/978-0-387-68979-1_7

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