Congenital and Developmental Diseases

  • J. Thomas Stocker


The pathology of infectious diseases of the lung is, for the most part, similar in adults and children. However, a number of other disorders either are seen almost exclusively in the pediatric age group (e.g., congenital anomalies) or occur in circumstances peculiar to this age group (e.g., hyaline membrane disease and bronchopulmonary dysplasia). Congenital anomalies of the lung are usually noted within the first weeks to months of life but may not be discovered until later in childhood or, in some cases such as bronchogenic cysts, until adulthood. A surprising number of new congenital anomalies have been described or further delineated since the last edition of this chapter, including alveolar capillary dysplasia, surfactant B deficiency, and two forms of congenital pulmonary airway malformation (previously called congenital cystic adenomatoid malformation).


Esophageal Atresia Pulmonary Hypoplasia Bronchogenic Cyst Congenital Cystic Adenomatoid Malformation Scimitar Syndrome 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media, LLC 2008

Authors and Affiliations

  • J. Thomas Stocker
    • 1
  1. 1.Uniformed Services University of the Health SciencesBethesda

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